{"id":79,"date":"2018-12-05T10:02:16","date_gmt":"2018-12-05T10:02:16","guid":{"rendered":"http:\/\/soignant.reseau-amylose.org\/?page_id=79"},"modified":"2026-06-12T16:18:42","modified_gmt":"2026-06-12T14:18:42","slug":"les-symptomes-cardiaques-et-extracardiaques-des-amyloses","status":"publish","type":"page","link":"https:\/\/reseau-amylose.org\/jesuissoignant\/pour-le-cardiologue\/les-symptomes-cardiaques-et-extracardiaques-des-amyloses\/","title":{"rendered":"Les sympt\u00f4mes cardiaques des amyloses"},"content":{"rendered":"\t\t<div data-elementor-type=\"wp-post\" data-elementor-id=\"79\" class=\"elementor elementor-79\" data-elementor-post-type=\"page\">\n\t\t\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-4ad9321f elementor-section-content-middle elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"4ad9321f\" data-element_type=\"section\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-no\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-1ed51128\" data-id=\"1ed51128\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-7e9939f elementor-widget elementor-widget-heading\" data-id=\"7e9939f\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h1 class=\"elementor-heading-title elementor-size-default\">Les sympt\u00f4mes cardiaques des amyloses<\/h1>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-7c9a6f10 elementor-widget-divider--view-line elementor-widget elementor-widget-divider\" data-id=\"7c9a6f10\" data-element_type=\"widget\" data-widget_type=\"divider.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-divider\">\n\t\t\t<span class=\"elementor-divider-separator\">\n\t\t\t\t\t\t<\/span>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-15702ac8 elementor-widget elementor-widget-heading\" data-id=\"15702ac8\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Manifestations cliniques \u00e0 l'usage du cardiologue \u00b7 R\u00e9seau Amylose \u00b7 Mis \u00e0 jour 2026<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-4635a931 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"4635a931\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-2af8596a\" data-id=\"2af8596a\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-c4061e6 elementor-widget elementor-widget-heading\" data-id=\"c4061e6\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Qu'est-ce que les manifestations cardiaques de l'amylose ?\n<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-7b74abed elementor-widget elementor-widget-text-editor\" data-id=\"7b74abed\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Les manifestations cardiaques de l&rsquo;amylose sont li\u00e9es aux d\u00e9p\u00f4ts amylo\u00efdes au sein du secteur interstitiel et des tissus nerveux myocardiques. Ces d\u00e9p\u00f4ts entra\u00eenent un \u00e9paississement progressif du myocarde, une alt\u00e9ration de la compliance ventriculaire et une dysfonction diastolique s\u00e9v\u00e8re, aboutissant \u00e0 une cardiomyopathie restrictive infiltrante.<\/p><p>Ces atteintes se traduisent cliniquement par des sympt\u00f4mes d&rsquo;insuffisance cardiaque et des troubles du rythme. L&rsquo;insuffisance cardiaque \u00e0 fraction d&rsquo;\u00e9jection pr\u00e9serv\u00e9e (FEVG \u2265 50 %) est la pr\u00e9sentation la plus fr\u00e9quente \u2014 elle est souvent \u00e9tiquet\u00e9e \u00e0 tort \u00ab cardiopathie hypertensive \u00bb ou \u00ab cardiomyopathie hypertrophique idiopathique \u00bb, retardant le diagnostic d&rsquo;amylose.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-e7ecda0 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"e7ecda0\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-15adaed\" data-id=\"15adaed\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-81b1967 elementor-widget elementor-widget-heading\" data-id=\"81b1967\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Poster - Quand penser \u00e0 l'amylose cardiaque ? <\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-f2b3458 elementor-widget elementor-widget-text-editor\" data-id=\"f2b3458\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<div class=\"poster-box\"><div class=\"pa\">Poster officiel du R\u00e9seau Amylose pr\u00e9sentant en 4 \u00e9tapes la d\u00e9marche diagnostique devant une suspicion d&rsquo;amylose cardiaque : suspicion clinique, signes extracardiaques, prescription des examens (scintigraphie + gammapathie) et orientation vers un centre expert.<\/div><div>\u00a0<\/div><div class=\"pauthors\"><span style=\"color: #808080\"><em>R\u00e9dig\u00e9 et relu par : T. Damy (Cr\u00e9teil), E. Donal (Rennes), A. Galat (Cr\u00e9teil), F. Hurson (Saint-Maur-des-Foss\u00e9s), O. Lairez (Toulouse), S. Oghina (Cr\u00e9teil) \u00b7 Avec le soutien institutionnel de Pfizer, Alnylam, Bayer, AstraZeneca<\/em><\/span><\/div><\/div>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-01d8d0f\" data-id=\"01d8d0f\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-d5081fd elementor-widget elementor-widget-image\" data-id=\"d5081fd\" data-element_type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img fetchpriority=\"high\" decoding=\"async\" width=\"725\" height=\"1024\" src=\"https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2026\/06\/Quand-penser-a-lamylose-image-725x1024.jpg\" class=\"attachment-large size-large wp-image-8285\" alt=\"Les sympt\u00f4mes cardiaques des amyloses\" srcset=\"https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2026\/06\/Quand-penser-a-lamylose-image-725x1024.jpg 725w, https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2026\/06\/Quand-penser-a-lamylose-image-212x300.jpg 212w, https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2026\/06\/Quand-penser-a-lamylose-image-768x1085.jpg 768w, https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2026\/06\/Quand-penser-a-lamylose-image.jpg 800w\" sizes=\"(max-width: 725px) 100vw, 725px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-34be498 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"34be498\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-fcc050e\" data-id=\"fcc050e\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-5287ace elementor-widget elementor-widget-heading\" data-id=\"5287ace\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">\u00c9tape 1 \u2014 Je suspecte une amylose cardiaque\n<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-c5e9a4a elementor-widget elementor-widget-heading\" data-id=\"c5e9a4a\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Devant ces pr\u00e9sentations cliniques :<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-52ab063 elementor-widget elementor-widget-text-editor\" data-id=\"52ab063\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li>Hypertrophie cardiaque (HVG) avec ou sans EPOF<\/li><li>Devant toute CMH + ou \u2013 EPOF<\/li><li>Insuffisance cardiaque \u00e0 FEVG pr\u00e9serv\u00e9e + HVG<\/li><li>Insuffisance cardiaque \u00e0 FEVG alt\u00e9r\u00e9e + HVG<\/li><li>Insuffisance cardiaque &gt; 65 ans + 1 red flag<\/li><li>Alt\u00e9ration du strain en cocarde + HVG<\/li><li>Devant EPOF (essoufflement, Prise de poids, Oed\u00e8mes, Fatigue)<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-1994ebd elementor-widget elementor-widget-heading\" data-id=\"1994ebd\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Devant ces anomalies cardiaques :<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-cd3ed16 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"cd3ed16\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-e5a382a\" data-id=\"e5a382a\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-b11c7ca elementor-widget elementor-widget-heading\" data-id=\"b11c7ca\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">ECG<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-c1785f7 elementor-widget elementor-widget-text-editor\" data-id=\"c1785f7\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li>Microvoltage<\/li><li>Onde Q pseudo-n\u00e9crose<\/li><li>Trouble de la conduction<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-32638a6\" data-id=\"32638a6\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-c44ae17 elementor-widget elementor-widget-heading\" data-id=\"c44ae17\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">\u00c9chocardiographie<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-8f951ba elementor-widget elementor-widget-text-editor\" data-id=\"8f951ba\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li>Hypertrophie biventriculaire (VG + VD)<\/li><li>Alt\u00e9ration du strain en cocarde<\/li><li>Anomalie de la fonction diastolique<\/li><li>Dilatation bi-atriale mod\u00e9r\u00e9e<\/li><li>Hyper\u00e9chog\u00e9nicit\u00e9 du myocarde<\/li><li>\u00c9paississement des valves (RA)<\/li><li>\u00c9paississement du septum inter-atria<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-f8f75cb\" data-id=\"f8f75cb\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-3e12093 elementor-widget elementor-widget-heading\" data-id=\"3e12093\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">IRM Cardiaque<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-9d3fd42 elementor-widget elementor-widget-text-editor\" data-id=\"9d3fd42\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li>Anomalies morphologiques<\/li><li>Rehaussement tardif diffus apr\u00e8s injection de gadolinium (VG, VD, OG, OD)<\/li><li>Difficult\u00e9 d&rsquo;annulation du myocarde sur le TI scouting<\/li><li>Augmentation du T1 Mapping<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-5947fba elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"5947fba\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-7a64727\" data-id=\"7a64727\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-0178b63 elementor-widget elementor-widget-heading\" data-id=\"0178b63\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">\u00c9tape 2 \u2014 Je recherche les signes extracardiaques<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-db60ceb elementor-widget elementor-widget-text-editor\" data-id=\"db60ceb\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Les signes extracardiaques aident au diagnostic et \u00e0 l&rsquo;orientation vers le type d&rsquo;amylose (AL, ATTRv ou ATTRwt). Les signes AL apparaissent souvent en moins de 2 ans ; les signes ATTR sauvage sont pr\u00e9sents depuis plus de 2 ans.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-bd9cf81 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"bd9cf81\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-3ac1732\" data-id=\"3ac1732\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-e0e3dd2 elementor-widget elementor-widget-heading\" data-id=\"e0e3dd2\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Signes en faveur d'une amylose AL (&lt; 2 ans)<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-05d0f1b elementor-widget elementor-widget-text-editor\" data-id=\"05d0f1b\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li>Macroglossie<\/li><li>Ecchymose p\u00e9ri-orbitaire<\/li><li>Purpura cutan\u00e9<\/li><li>L\u00e9sions ungu\u00e9ales<\/li><li>Dysphagie<\/li><li>Dysautonomie vasculaire<\/li><li>Dysautonomie dygestive : naus\u00e9es, vomissements, diarrh\u00e9es, constipation<\/li><li>Perte de poids importante<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-7532035\" data-id=\"7532035\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-1e55cb5 elementor-widget elementor-widget-heading\" data-id=\"1e55cb5\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">Signes communs : atteinte cardiaque EPOF<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-14bea3d elementor-widget elementor-widget-text-editor\" data-id=\"14bea3d\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li><b>E<\/b>ssoufflement<\/li><li><strong>P<\/strong>rise de poids<\/li><li><strong>O<\/strong>ed\u00e8mes<\/li><li><strong>F<\/strong>atigue<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-c4296ab\" data-id=\"c4296ab\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-d7720cb elementor-widget elementor-widget-heading\" data-id=\"d7720cb\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Signes en faveur d'une \u00e0 transthyr\u00e9tine h\u00e9r\u00e9ditaire sauvage ATTRwt (&gt; 2 ans)<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-d945da7 elementor-widget elementor-widget-text-editor\" data-id=\"d945da7\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li>Canal Carpien<\/li><li>Doigt \u00e0 Ressaut ou Dupuytren\u00a0<b>(rajouter Dupuytren)<\/b><\/li><li><b><\/b>Rupture tendineuse\u00a0<b>(\u00e9paule, biceps, achille)<\/b><\/li><li><b><\/b>Arthrose (<b>retirer RAPIDE)<\/b><\/li><li><b><\/b>Proth\u00e8se de Hanche et de Genou<\/li><li>Canal\u00a0<b>lombaire ou cervical<\/b>\u00a0r\u00e9tr\u00e9ci<\/li><li>Surdit\u00e9<\/li><li>PTH et\/ou PTG<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-4f93f34 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"4f93f34\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-a2da695\" data-id=\"a2da695\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-15805e2 elementor-widget elementor-widget-heading\" data-id=\"15805e2\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Tous les signes sont en faveur d'une amylose \u00e0 transthyr\u00e9tine h\u00e9r\u00e9ditaire ATTRv<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-c75eefb elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"c75eefb\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-0696db2\" data-id=\"0696db2\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-6296f3d elementor-widget elementor-widget-heading\" data-id=\"6296f3d\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">\u00c9tape 3 \u2014 Je prescris scintigraphie + gammapathie<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-d63482b elementor-widget elementor-widget-text-editor\" data-id=\"d63482b\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Ces deux examens sont prescrits\u00a0<strong>simultan\u00e9ment<\/strong> d\u00e8s la suspicion d&rsquo;amylose cardiaque. La scintigraphie ne peut pas \u00eatre interpr\u00e9t\u00e9e sans les r\u00e9sultats de la gammapathie.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-825a324 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"825a324\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-37527bc\" data-id=\"37527bc\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-e212f2a elementor-widget elementor-widget-heading\" data-id=\"e212f2a\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">Scintigraphie osseuse<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-56e32c5 elementor-widget elementor-widget-text-editor\" data-id=\"56e32c5\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<div class=\"clin-card\"><ul><li>Fixation intense et diffuse au c\u0153ur = \u00e9vocatrice d&rsquo;amylose TTR<\/li><li>Absence de fixation cardiaque = en faveur d&rsquo;amylose AL en cas d&rsquo;\u00e9chocardiogrpahie ou d&rsquo;IRM suspectant une cardiopathie amylo\u00efde<\/li><li>Calcul du score de Perugini ou ratio c\u0153ur\/SPECT<\/li><\/ul><\/div>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-e438844\" data-id=\"e438844\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-dd445f4 elementor-widget elementor-widget-heading\" data-id=\"dd445f4\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">Gammapathies<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-6a4bd8a elementor-widget elementor-widget-text-editor\" data-id=\"6a4bd8a\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li>\u00c9lectrophor\u00e8se des prot\u00e9ines s\u00e9riques (EPP)<\/li><li>Immunofixation des s\u00e9riques<\/li><li>Dosage des cha\u00eenes l\u00e9g\u00e8res libres (CLL) kappa et lambda (<span class=\"s1\">K<\/span> et <span class=\"s1\">\u03bb) <\/span>s\u00e9riques<\/li><li>Prot\u00e9inurie de Bence-Jones urinaire (=CLL urinaires)<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-567a37f elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"567a37f\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-4031f85\" data-id=\"4031f85\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-eed67d1 elementor-align-center elementor-widget elementor-widget-button\" data-id=\"eed67d1\" data-element_type=\"widget\" data-widget_type=\"button.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<div class=\"elementor-button-wrapper\">\n\t\t\t\t\t<a class=\"elementor-button elementor-button-link elementor-size-sm\" href=\"https:\/\/reseau-amylose.org\/jesuissoignant\/ordonnances-amylose-cardiaque-consultations\/\" target=\"_blank\">\n\t\t\t\t\t\t<span class=\"elementor-button-content-wrapper\">\n\t\t\t\t\t\t\t\t\t<span class=\"elementor-button-text\">T\u00e9l\u00e9chargez les ordonnances type pour ces examens<\/span>\n\t\t\t\t\t<\/span>\n\t\t\t\t\t<\/a>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-88c1183 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"88c1183\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-37951f1\" data-id=\"37951f1\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-fcf8ae9 elementor-widget elementor-widget-heading\" data-id=\"fcf8ae9\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">\u00c9tape 4 \u2014 Je m'oriente vers un centre expert<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-f2f741d elementor-widget elementor-widget-text-editor\" data-id=\"f2f741d\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>En urgence, en cas de suspicion d&rsquo;amylose AL (preuve histologique et traitement) et pour toutes les ATTR : r\u00e9alisation du test g\u00e9n\u00e9tique et initiation du traitement sp\u00e9cifique.<\/p><p>Pour trouver le centre expert le plus proche, consulter notre page R\u00e9seau de soin Amylose National sur la page suivante <a href=\"https:\/\/reseau-amylose.org\/soins\/reseau-amylose-national-france\/\" target=\"_blank\" rel=\"noopener\">CLIQUEZ ICI<\/a><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-9bd4828 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"9bd4828\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-66 elementor-top-column elementor-element elementor-element-d751f0a\" data-id=\"d751f0a\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-6aef4e2 elementor-widget elementor-widget-text-editor\" data-id=\"6aef4e2\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<h3><strong><span style=\"color: #4db8f0\">Chez qui suspecter une amylose en consultation et quel int\u00e9r\u00eat ? Une course contre le temps<\/span><\/strong><\/h3><h4><em><span style=\"color: #4db8f0\">Pierre SABOURET<\/span><\/em><\/h4>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-3bd5c95 elementor-widget elementor-widget-video\" data-id=\"3bd5c95\" data-element_type=\"widget\" data-settings=\"{&quot;youtube_url&quot;:&quot;https:\\\/\\\/www.youtube.com\\\/watch?v=SEuzb-6rDec&amp;list=PLgcbJqP0xnzjk0ZXZFG83enHJBWuFAdjq&amp;index=2&amp;ab_channel=R%C3%A9seauAmyloseR%C3%A9seauAmylose&quot;,&quot;video_type&quot;:&quot;youtube&quot;,&quot;controls&quot;:&quot;yes&quot;}\" data-widget_type=\"video.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-wrapper elementor-open-inline\">\n\t\t\t<div class=\"elementor-video\"><\/div>\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-4265c01\" data-id=\"4265c01\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap\">\n\t\t\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-2ac39a8 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"2ac39a8\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-8b295c8\" data-id=\"8b295c8\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-4405b87 elementor-widget elementor-widget-heading\" data-id=\"4405b87\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">FAQ \u2014 Quand penser \u00e0 l'amylose cardiaque ?<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-a3d1a0b elementor-widget elementor-widget-toggle\" data-id=\"a3d1a0b\" data-element_type=\"widget\" data-widget_type=\"toggle.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-toggle\">\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1711\" class=\"elementor-tab-title\" data-tab=\"1\" role=\"button\" aria-controls=\"elementor-tab-content-1711\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-left\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Quels sont les signes cliniques qui doivent faire suspecter une amylose cardiaque ?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1711\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"1\" role=\"region\" aria-labelledby=\"elementor-tab-title-1711\"><div class=\"fq\"><div class=\"fq-a\">Toute HVG inexpliqu\u00e9e, insuffisance cardiaque \u00e0 FEVG pr\u00e9serv\u00e9e, CMH, r\u00e9tr\u00e9cissement aortique, trouble de la conduction ou alt\u00e9ration du strain en cocarde \u00e0 l&rsquo;\u00e9chocardiographie doivent faire \u00e9voquer une amylose cardiaque, surtout si associ\u00e9s \u00e0 des signes extracardiaques.<\/div><\/div><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1712\" class=\"elementor-tab-title\" data-tab=\"2\" role=\"button\" aria-controls=\"elementor-tab-content-1712\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-left\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Quels signes extracardiaques orientent vers une amylose AL ?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1712\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"2\" role=\"region\" aria-labelledby=\"elementor-tab-title-1712\"><div class=\"fq-q\">Les signes \u00e9vocateurs d&rsquo;amylose AL (pr\u00e9sents en moins de 2 ans) incluent : macroglossie, ecchymose p\u00e9ri-orbitaire, purpura cutan\u00e9, neuropathie, dysautonomie vasculaire et digestive, perte de poids importante.<\/div><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1713\" class=\"elementor-tab-title\" data-tab=\"3\" role=\"button\" aria-controls=\"elementor-tab-content-1713\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-left\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Quels signes extracardiaques orientent vers une amylose ATTR sauvage ?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1713\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"3\" role=\"region\" aria-labelledby=\"elementor-tab-title-1713\"><p>Les signes \u00e9vocateurs d&rsquo;amylose ATTRwt (pr\u00e9sents depuis plus de 2 ans) se sybolysent par R&rsquo;EPOF : atteintes rhumatologiques : canal carpien bilat\u00e9ral, doigt \u00e0 ressaut, rupture du tendon long biceps, rupture de la coiffe des rotateurs, canal lombaire \u00e9troit, Surdit\u00e9 et les signes EPOF de l&rsquo;insuffisance cardiaque (Essoufflment Prise de poids Oed\u00e8mes, Fatigue).<\/p><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1714\" class=\"elementor-tab-title\" data-tab=\"4\" role=\"button\" aria-controls=\"elementor-tab-content-1714\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-left\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Pourquoi prescrire scintigraphie et gammapathie simultan\u00e9ment ?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1714\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"4\" role=\"region\" aria-labelledby=\"elementor-tab-title-1714\"><div class=\"fq\"><div class=\"fq-a\">La scintigraphie osseuse ne peut pas \u00eatre interpr\u00e9t\u00e9e sans le r\u00e9sultat de la gammapathie. Une fixation cardiaque intense associ\u00e9e \u00e0 l&rsquo;absence de gammapathie est tr\u00e8s \u00e9vocatrice d&rsquo;amylose ATTR. En cas de gammapathie, le bilan doit \u00eatre compl\u00e9t\u00e9 par une biopsie avant tout traitement. Les deux examens sont donc indissociables.<\/div><\/div><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1715\" class=\"elementor-tab-title\" data-tab=\"5\" role=\"button\" aria-controls=\"elementor-tab-content-1715\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-left\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Quand orienter en urgence vers un centre expert ?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1715\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"5\" role=\"region\" aria-labelledby=\"elementor-tab-title-1715\"><p>En urgence d\u00e8s la suspicion d&rsquo;amylose AL, car le traitement (chimioth\u00e9rapie) doit \u00eatre initi\u00e9 rapidement. Pour toutes les ATTR, pour la r\u00e9alisation du test g\u00e9n\u00e9tique et l&rsquo;initiation du traitement sp\u00e9cifique<\/p><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-0d3b5f2 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"0d3b5f2\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-8b8a024\" data-id=\"8b8a024\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-ba2bfdf elementor-widget elementor-widget-text-editor\" data-id=\"ba2bfdf\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>L&rsquo;amylose cardiaque doit \u00eatre suspect\u00e9e devant toute HVG inexpliqu\u00e9e, insuffisance cardiaque \u00e0 FEVG pr\u00e9serv\u00e9e, CMH, r\u00e9tr\u00e9cissement aortique, trouble de la conduction ou alt\u00e9ration du strain en cocarde \u00e0 l&rsquo;\u00e9chocardiographie. Les signes extracardiaques orientent vers le type : macroglossie, ecchymose p\u00e9ri-orbitaire, neuropathie pour l&rsquo;amylose AL (signes r\u00e9cents &lt; 2 ans) ; canal carpien, surdit\u00e9, rupture tendineuse pour l&rsquo;amylose ATTR sauvage (signes anciens &gt; 2 ans). La d\u00e9marche diagnostique impose la prescription simultan\u00e9e d&rsquo;une scintigraphie osseuse et d&rsquo;une recherche de gammapathie (4 tests : EPP, immunofixation, CLL s\u00e9riques, Bence-Jones urinaires). En cas de suspicion d&rsquo;AL ou d&rsquo;ATTR, adresser en urgence au centre expert.\u00a0<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<\/div>\n\t\t","protected":false},"excerpt":{"rendered":"<p>Les sympt\u00f4mes cardiaques des amyloses Manifestations cliniques \u00e0 l&rsquo;usage du cardiologue \u00b7 R\u00e9seau Amylose \u00b7 Mis \u00e0 jour 2026 Qu&rsquo;est-ce que les manifestations cardiaques de l&rsquo;amylose ? Les manifestations cardiaques de l&rsquo;amylose sont li\u00e9es aux d\u00e9p\u00f4ts amylo\u00efdes au sein du secteur interstitiel et des tissus nerveux myocardiques. Ces d\u00e9p\u00f4ts entra\u00eenent un \u00e9paississement progressif du myocarde, [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"parent":115,"menu_order":3,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_acf_changed":false,"footnotes":""},"categories":[],"tags":[],"class_list":["post-79","page","type-page","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v25.5 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Les sympt\u00f4mes cardiaques des amyloses - R\u00e9seau Amylose<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/reseau-amylose.org\/jesuissoignant\/pour-le-cardiologue\/les-symptomes-cardiaques-et-extracardiaques-des-amyloses\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Les sympt\u00f4mes cardiaques des amyloses - R\u00e9seau Amylose\" \/>\n<meta property=\"og:description\" content=\"Les sympt\u00f4mes cardiaques des amyloses Manifestations cliniques \u00e0 l&rsquo;usage du cardiologue \u00b7 R\u00e9seau Amylose \u00b7 Mis \u00e0 jour 2026 Qu&rsquo;est-ce que les manifestations cardiaques de l&rsquo;amylose ? Les manifestations cardiaques de l&rsquo;amylose sont li\u00e9es aux d\u00e9p\u00f4ts amylo\u00efdes au sein du secteur interstitiel et des tissus nerveux myocardiques. Ces d\u00e9p\u00f4ts entra\u00eenent un \u00e9paississement progressif du myocarde, [&hellip;]\" \/>\n<meta property=\"og:url\" content=\"https:\/\/reseau-amylose.org\/jesuissoignant\/pour-le-cardiologue\/les-symptomes-cardiaques-et-extracardiaques-des-amyloses\/\" \/>\n<meta property=\"og:site_name\" content=\"R\u00e9seau Amylose\" \/>\n<meta property=\"article:modified_time\" content=\"2026-06-12T14:18:42+00:00\" \/>\n<meta property=\"og:image\" content=\"https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2026\/06\/Quand-penser-a-lamylose-image-725x1024.jpg\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Dur\u00e9e de lecture estim\u00e9e\" \/>\n\t<meta name=\"twitter:data1\" content=\"6 minutes\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\/\/schema.org\",\"@graph\":[{\"@type\":\"WebPage\",\"@id\":\"https:\/\/reseau-amylose.org\/jesuissoignant\/pour-le-cardiologue\/les-symptomes-cardiaques-et-extracardiaques-des-amyloses\/\",\"url\":\"https:\/\/reseau-amylose.org\/jesuissoignant\/pour-le-cardiologue\/les-symptomes-cardiaques-et-extracardiaques-des-amyloses\/\",\"name\":\"Les sympt\u00f4mes cardiaques des amyloses - R\u00e9seau Amylose\",\"isPartOf\":{\"@id\":\"https:\/\/reseau-amylose.org\/jesuissoignant\/#website\"},\"primaryImageOfPage\":{\"@id\":\"https:\/\/reseau-amylose.org\/jesuissoignant\/pour-le-cardiologue\/les-symptomes-cardiaques-et-extracardiaques-des-amyloses\/#primaryimage\"},\"image\":{\"@id\":\"https:\/\/reseau-amylose.org\/jesuissoignant\/pour-le-cardiologue\/les-symptomes-cardiaques-et-extracardiaques-des-amyloses\/#primaryimage\"},\"thumbnailUrl\":\"https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2026\/06\/Quand-penser-a-lamylose-image-725x1024.jpg\",\"datePublished\":\"2018-12-05T10:02:16+00:00\",\"dateModified\":\"2026-06-12T14:18:42+00:00\",\"breadcrumb\":{\"@id\":\"https:\/\/reseau-amylose.org\/jesuissoignant\/pour-le-cardiologue\/les-symptomes-cardiaques-et-extracardiaques-des-amyloses\/#breadcrumb\"},\"inLanguage\":\"fr-FR\",\"potentialAction\":[{\"@type\":\"ReadAction\",\"target\":[\"https:\/\/reseau-amylose.org\/jesuissoignant\/pour-le-cardiologue\/les-symptomes-cardiaques-et-extracardiaques-des-amyloses\/\"]}]},{\"@type\":\"ImageObject\",\"inLanguage\":\"fr-FR\",\"@id\":\"https:\/\/reseau-amylose.org\/jesuissoignant\/pour-le-cardiologue\/les-symptomes-cardiaques-et-extracardiaques-des-amyloses\/#primaryimage\",\"url\":\"https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2026\/06\/Quand-penser-a-lamylose-image.jpg\",\"contentUrl\":\"https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2026\/06\/Quand-penser-a-lamylose-image.jpg\",\"width\":800,\"height\":1130,\"caption\":\"Les sympt\u00f4mes cardiaques des amyloses\"},{\"@type\":\"BreadcrumbList\",\"@id\":\"https:\/\/reseau-amylose.org\/jesuissoignant\/pour-le-cardiologue\/les-symptomes-cardiaques-et-extracardiaques-des-amyloses\/#breadcrumb\",\"itemListElement\":[{\"@type\":\"ListItem\",\"position\":1,\"name\":\"Accueil\",\"item\":\"https:\/\/reseau-amylose.org\/jesuissoignant\/\"},{\"@type\":\"ListItem\",\"position\":2,\"name\":\"Pour le cardiologue\",\"item\":\"https:\/\/reseau-amylose.org\/jesuissoignant\/pour-le-cardiologue\/\"},{\"@type\":\"ListItem\",\"position\":3,\"name\":\"Les sympt\u00f4mes cardiaques des amyloses\"}]},{\"@type\":\"WebSite\",\"@id\":\"https:\/\/reseau-amylose.org\/jesuissoignant\/#website\",\"url\":\"https:\/\/reseau-amylose.org\/jesuissoignant\/\",\"name\":\"R\u00e9seau Amylose\",\"description\":\"Centre de r\u00e9f\u00e9rence des amyloses cardiaques espace soignant\",\"potentialAction\":[{\"@type\":\"SearchAction\",\"target\":{\"@type\":\"EntryPoint\",\"urlTemplate\":\"https:\/\/reseau-amylose.org\/jesuissoignant\/?s={search_term_string}\"},\"query-input\":{\"@type\":\"PropertyValueSpecification\",\"valueRequired\":true,\"valueName\":\"search_term_string\"}}],\"inLanguage\":\"fr-FR\"}]}<\/script>\n<!-- \/ Yoast SEO plugin. -->","yoast_head_json":{"title":"Les sympt\u00f4mes cardiaques des amyloses - R\u00e9seau Amylose","robots":{"index":"index","follow":"follow","max-snippet":"max-snippet:-1","max-image-preview":"max-image-preview:large","max-video-preview":"max-video-preview:-1"},"canonical":"https:\/\/reseau-amylose.org\/jesuissoignant\/pour-le-cardiologue\/les-symptomes-cardiaques-et-extracardiaques-des-amyloses\/","og_locale":"fr_FR","og_type":"article","og_title":"Les sympt\u00f4mes cardiaques des amyloses - R\u00e9seau Amylose","og_description":"Les sympt\u00f4mes cardiaques des amyloses Manifestations cliniques \u00e0 l&rsquo;usage du cardiologue \u00b7 R\u00e9seau Amylose \u00b7 Mis \u00e0 jour 2026 Qu&rsquo;est-ce que les manifestations cardiaques de l&rsquo;amylose ? 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