{"id":5525,"date":"2022-07-18T11:10:51","date_gmt":"2022-07-18T09:10:51","guid":{"rendered":"https:\/\/reseau-amylose.org\/jesuissoignant\/?page_id=5525"},"modified":"2026-08-26T10:01:05","modified_gmt":"2026-08-26T08:01:05","slug":"pour-le-medecin-generaliste","status":"publish","type":"page","link":"https:\/\/reseau-amylose.org\/jesuissoignant\/pour-le-medecin-generaliste\/","title":{"rendered":"Pour le M\u00e9decin G\u00e9n\u00e9raliste"},"content":{"rendered":"\t\t<div data-elementor-type=\"wp-page\" data-elementor-id=\"5525\" class=\"elementor elementor-5525\" data-elementor-post-type=\"page\">\n\t\t\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-39559bc7 elementor-section-content-middle elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"39559bc7\" data-element_type=\"section\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-no\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-3749cbbb\" data-id=\"3749cbbb\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-2e44f7c elementor-widget elementor-widget-heading\" data-id=\"2e44f7c\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h1 class=\"elementor-heading-title elementor-size-default\">Pour le M\u00e9decin G\u00e9n\u00e9raliste<\/h1>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-625be1a4 elementor-widget-divider--view-line elementor-widget elementor-widget-divider\" data-id=\"625be1a4\" data-element_type=\"widget\" data-widget_type=\"divider.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-divider\">\n\t\t\t<span class=\"elementor-divider-separator\">\n\t\t\t\t\t\t<\/span>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-cda7b3b elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"cda7b3b\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-4da1970\" data-id=\"4da1970\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-3c44ae6 elementor-widget elementor-widget-text-editor\" data-id=\"3c44ae6\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Les amyloses cardiaques sont des maladies rares et syst\u00e9miques, entra\u00eenant le d\u00e9p\u00f4t de fibrilles amylo\u00efdes dans les organes atteints. Ces organes sont principalement le c\u0153ur, mais \u00e9galement les t\u00e9guments, les reins, le syst\u00e8me nerveux p\u00e9riph\u00e9rique et v\u00e9g\u00e9tatif, le tractus gastro-intestinal et le syst\u00e8me ORL. Cette maladie atteint quasi exclusivement les adultes.<\/p><p>Il existe trois formes d&rsquo;amyloses cardiaques : AL (\u00e0 cha\u00eenes l\u00e9g\u00e8res d&rsquo;immunoglobuline), ATTR sauvage (\u00e0 transthyr\u00e9tine sauvage \u2013 ATTRwt), et ATTRv (transthyr\u00e9tine mut\u00e9e). Les sympt\u00f4mes peuvent \u00eatre cardiaques et extracardiaques et sont variables d&rsquo;une forme \u00e0 l&rsquo;autre et d&rsquo;un individu \u00e0 l&rsquo;autre, rendant le diagnostic difficile du fait de l&rsquo;h\u00e9t\u00e9rog\u00e9n\u00e9it\u00e9 des ph\u00e9notypes.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-61756f8 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"61756f8\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-ca1c989\" data-id=\"ca1c989\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-f871068 elementor-widget elementor-widget-heading\" data-id=\"f871068\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Points cl\u00e9s pour les professionnels de sant\u00e9<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-0db95e0 elementor-widget elementor-widget-text-editor\" data-id=\"0db95e0\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li>Trois formes d&rsquo;amylose cardiaque : AL, ATTR sauvage (ATTRwt) et ATTR h\u00e9r\u00e9ditaire (mut\u00e9e, ATTRv).<\/li><li>Les amyloses cardiaques miment de nombreux ph\u00e9notypes cardiaques classiques, source d&rsquo;errance diagnostique.<\/li><li>Les manifestations extracardiaques (canal carpien, ORL, dysautonomie, neuropathie, syndrome n\u00e9phrotique) sont des \u00ab red flags \u00bb pouvant pr\u00e9c\u00e9der l&rsquo;atteinte cardiaque.<\/li><li>La prise en charge est une urgence, en particulier pour l&rsquo;amylose AL, \u00e0 \u00e9volution rapide.<\/li><li>Toute suspicion doit conduire \u00e0 adresser le patient \u00e0 un centre de r\u00e9f\u00e9rence ou de comp\u00e9tence du R\u00e9seau Amylose.<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-a09abeb elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"a09abeb\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-84276ca\" data-id=\"84276ca\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-cd33096 elementor-widget elementor-widget-heading\" data-id=\"cd33096\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Manifestations cardiaques<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-31eeb6a elementor-widget elementor-widget-text-editor\" data-id=\"31eeb6a\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>L&rsquo;infiltration amylo\u00efde cardiaque peut toucher toutes les tuniques cardiaques : myocarde, endocarde (valves), p\u00e9ricarde et tissu \u00e9lectrique. Ce processus infiltratif est dynamique, et rapidement \u00e9volutif en l&rsquo;absence de traitement.<\/p><p>Le ph\u00e9notype cardiaque d\u00e9pend du degr\u00e9 d&rsquo;infiltration de ces tuniques : \u00e9paississement des parois du c\u0153ur, troubles conductifs ou rythmiques, alt\u00e9ration des fonctions diastolique et systolique.<\/p><p><strong>L&rsquo;errance diagnostique <\/strong>est li\u00e9e au fait que les amyloses cardiaques miment les ph\u00e9notypes des syndromes cardiaques suivants :<\/p><ul><li>Cardiomyopathie hypertrophique.<\/li><li>Insuffisance cardiaque \u00e0 fraction d&rsquo;\u00e9jection du ventricule gauche pr\u00e9serv\u00e9e.<\/li><li>Insuffisance cardiaque \u00e0 fraction d&rsquo;\u00e9jection du ventricule gauche alt\u00e9r\u00e9e avec hypertrophie myocardique.<\/li><li>Hypertrophie ventriculaire gauche avec bloc de branche, BAV 2-3, fibrillation atriale ou flutter.<\/li><li>R\u00e9tr\u00e9cissement aortique calcifi\u00e9 avec hypertrophie ventriculaire gauche, ou bas d\u00e9bit\/bas gradient.<\/li><\/ul><p>Les sympt\u00f4mes communs aux diff\u00e9rentes formes d&rsquo;amylose cardiaque sont ceux de l&rsquo;insuffisance cardiaque (essoufflement, prise de poids, \u0153d\u00e8mes et fatigue \u2014 EPOF) et des troubles du rythme et de la conduction (palpitations, vertige, syncope).<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-00fb2e9 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"00fb2e9\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-19e6a13\" data-id=\"19e6a13\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-4949df4 elementor-widget elementor-widget-heading\" data-id=\"4949df4\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Manifestations extracardiaques<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-4c48705 elementor-widget elementor-widget-text-editor\" data-id=\"4c48705\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>L&rsquo;infiltration amylo\u00efde peut toucher de nombreux organes. Ces atteintes peuvent pr\u00e9c\u00e9der l&rsquo;atteinte cardiaque et servir de \u00ab red flag \u00bb.<\/p><p><strong>Atteintes t\u00e9gumentaires : <\/strong>infiltration des canaux carpiens, canal lombaire, canal cervical, maladie de Dupuytren.<\/p><p><strong>Atteintes ORL : <\/strong>surdit\u00e9, dysphagie, macroglossie, dysphonie.<\/p><p><strong>Atteintes dysautonomiques : <\/strong>hypotension art\u00e9rielle, gastropar\u00e9sie, diarrh\u00e9es, constipation, dysfonction urinaire.<\/p><p><strong>Neuropathie p\u00e9riph\u00e9rique.<\/strong><\/p><p><strong>Syndrome n\u00e9phrotique.<\/strong><\/p><p><strong>Alt\u00e9ration de l&rsquo;\u00e9tat g\u00e9n\u00e9ral : <\/strong>d\u00e9nutrition (perte de poids), fatigue.<\/p><p><strong>Autres : <\/strong>atteinte h\u00e9patique (h\u00e9patom\u00e9galie, cholestase et cytolyse), atteinte pulmonaire, prostate\u2026<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-2fd40fe elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"2fd40fe\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-262e50c\" data-id=\"262e50c\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-01ee1d7 elementor-widget elementor-widget-heading\" data-id=\"01ee1d7\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Conduite \u00e0 tenir par le m\u00e9decin traitant<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-83538a9 elementor-widget elementor-widget-text-editor\" data-id=\"83538a9\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>La prise en charge des amyloses cardiaques est une urgence car il s&rsquo;agit d&rsquo;une pathologie \u00e0 \u00e9volution rapide, et encore plus particuli\u00e8rement dans le cas des amyloses AL.<\/p><p>En cas de suspicion d&rsquo;amylose cardiaque, le m\u00e9decin traitant ou le cardiologue adressera son patient \u00e0 un des centres du R\u00e9seau Amylose.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-d12ba5e elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"d12ba5e\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-33af32b\" data-id=\"33af32b\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-23f4c1b elementor-widget elementor-widget-heading\" data-id=\"23f4c1b\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Protocole National de Diagnostic et de Soins (PNDS)<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-9ec751d elementor-widget elementor-widget-text-editor\" data-id=\"9ec751d\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<h4><span style=\"text-decoration: underline\"><strong><span style=\"color: #000000;text-decoration: underline\">Protocole National de Diagnostic et de Soins<\/span><\/strong><\/span><\/h4><h6><span style=\"color: #000000\">T\u00e9l\u00e9chargez ci-dessous la synth\u00e8se de ce document \u00e0 destination du m\u00e9decin traitant :\u00a0<\/span><\/h6>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-019b238 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"019b238\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-16 elementor-top-column elementor-element elementor-element-36abf86\" data-id=\"36abf86\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap\">\n\t\t\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-66 elementor-top-column elementor-element elementor-element-d038f82\" data-id=\"d038f82\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-a2e3123 elementor-cta--skin-cover elementor-animated-content elementor-bg-transform elementor-bg-transform-zoom-in elementor-widget elementor-widget-call-to-action\" data-id=\"a2e3123\" data-element_type=\"widget\" data-widget_type=\"call-to-action.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<a class=\"elementor-cta\" href=\"https:\/\/www.has-sante.fr\/upload\/docs\/application\/pdf\/2021-12\/synthese_mg_amylose_cardiaque.pdf\" target=\"_blank\">\n\t\t\t\t\t<div class=\"elementor-cta__bg-wrapper\">\n\t\t\t\t<div class=\"elementor-cta__bg elementor-bg\" style=\"background-image: url(https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2022\/07\/Capture-de\u0301cran-2022-07-18-a\u0300-11.31.46-1024x501.png);\" role=\"img\" aria-label=\"Capture d\u2019e\u0301cran 2022-07-18 a\u0300 11.31.46\"><\/div>\n\t\t\t\t<div class=\"elementor-cta__bg-overlay\"><\/div>\n\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-cta__content\">\n\t\t\t\t\n\t\t\t\t\n\t\t\t\t\n\t\t\t\t\t\t\t\t\t<div class=\"elementor-cta__button-wrapper elementor-cta__content-item elementor-content-item elementor-animated-item--grow\">\n\t\t\t\t\t<span class=\"elementor-cta__button elementor-button elementor-size-lg\">\n\t\t\t\t\t\tCliquez ici\t\t\t\t\t<\/span>\n\t\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\t\t<\/a>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-16 elementor-top-column elementor-element elementor-element-1293ed5\" data-id=\"1293ed5\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap\">\n\t\t\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-aa649b4 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"aa649b4\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-c6073e4\" data-id=\"c6073e4\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap\">\n\t\t\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-06f1cb7\" data-id=\"06f1cb7\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-129d67c elementor-align-center elementor-widget elementor-widget-button\" data-id=\"129d67c\" data-element_type=\"widget\" data-widget_type=\"button.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<div class=\"elementor-button-wrapper\">\n\t\t\t\t\t<a class=\"elementor-button elementor-button-link elementor-size-md\" href=\"https:\/\/reseau-amylose.org\/jesuissoignant\/pnds-amyloses-cardiaques\/https:\/\/reseau-amylose.org\/jesuissoignant\/pnds-amyloses-cardiaques\/\" target=\"_blank\">\n\t\t\t\t\t\t<span class=\"elementor-button-content-wrapper\">\n\t\t\t\t\t\t\t\t\t<span class=\"elementor-button-text\">T\u00e9l\u00e9chargez le Protocole National de Diagnostic et de Soins dans son int\u00e9gralit\u00e9 ICI<\/span>\n\t\t\t\t\t<\/span>\n\t\t\t\t\t<\/a>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-f1c6a25 elementor-widget elementor-widget-text-editor\" data-id=\"f1c6a25\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><span style=\"color: #808080\"><em>Document \u00e9labor\u00e9 par le Centre de R\u00e9f\u00e9rence Amyloses Cardiaques (H\u00f4pital Henri-Mondor, APHP) de la Fili\u00e8re Nationale de sant\u00e9 Cardiogen selon la m\u00e9thodologie de la HAS, sert de r\u00e9f\u00e9rence pour la prise en charge.<\/em><\/span><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-31b3471\" data-id=\"31b3471\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap\">\n\t\t\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-1552647 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"1552647\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-b9dec66\" data-id=\"b9dec66\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-767f449 elementor-widget elementor-widget-heading\" data-id=\"767f449\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">FAQ \u2014 Questions fr\u00e9quentes<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-8a1ae50 elementor-widget elementor-widget-toggle\" data-id=\"8a1ae50\" data-element_type=\"widget\" data-widget_type=\"toggle.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-toggle\">\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1441\" class=\"elementor-tab-title\" data-tab=\"1\" role=\"button\" aria-controls=\"elementor-tab-content-1441\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-left\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Quelles sont les trois formes d'amylose cardiaque ?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1441\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"1\" role=\"region\" aria-labelledby=\"elementor-tab-title-1441\"><p>L&rsquo;amylose AL (\u00e0 cha\u00eenes l\u00e9g\u00e8res d&rsquo;immunoglobuline), l&rsquo;amylose ATTR sauvage (ATTRwt) et l&rsquo;amylose ATTR h\u00e9r\u00e9ditaire (mut\u00e9e).<\/p><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1442\" class=\"elementor-tab-title\" data-tab=\"2\" role=\"button\" aria-controls=\"elementor-tab-content-1442\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-left\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Pourquoi le diagnostic de l'amylose cardiaque est-il souvent retard\u00e9 ?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1442\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"2\" role=\"region\" aria-labelledby=\"elementor-tab-title-1442\"><p>Parce qu&rsquo;elle mime de nombreux ph\u00e9notypes cardiaques classiques (cardiomyopathie hypertrophique, insuffisance cardiaque \u00e0 FEVG pr\u00e9serv\u00e9e ou alt\u00e9r\u00e9e, r\u00e9tr\u00e9cissement aortique) et que ses manifestations extracardiaques sont souvent m\u00e9connues comme signes d&rsquo;alerte.<\/p><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1443\" class=\"elementor-tab-title\" data-tab=\"3\" role=\"button\" aria-controls=\"elementor-tab-content-1443\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-left\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Quels signes extracardiaques doivent alerter le m\u00e9decin g\u00e9n\u00e9raliste ?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1443\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"3\" role=\"region\" aria-labelledby=\"elementor-tab-title-1443\"><p>Un syndrome du canal carpien, une surdit\u00e9 ou une dysphagie inexpliqu\u00e9es, une dysautonomie, une neuropathie p\u00e9riph\u00e9rique ou un syndrome n\u00e9phrotique, en particulier associ\u00e9s entre eux.<\/p><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1444\" class=\"elementor-tab-title\" data-tab=\"4\" role=\"button\" aria-controls=\"elementor-tab-content-1444\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-left\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Que faire en cas de suspicion d'amylose cardiaque ?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1444\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"4\" role=\"region\" aria-labelledby=\"elementor-tab-title-1444\"><p>Adresser le patient \u00e0 un centre de r\u00e9f\u00e9rence ou de comp\u00e9tence de la fili\u00e8re Cardiogen, la prise en charge \u00e9tant une urgence, en particulier pour l&rsquo;amylose AL.<\/p><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-67c5160 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"67c5160\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-3e9090c\" data-id=\"3e9090c\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-0623b25 elementor-widget elementor-widget-text-editor\" data-id=\"0623b25\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>L&rsquo;amylose cardiaque regroupe trois formes principales \u2014 AL, ATTR sauvage (ATTRwt) et ATTR h\u00e9r\u00e9ditaire (ATTRv) \u2014 caract\u00e9ris\u00e9es par le d\u00e9p\u00f4t de fibrilles amylo\u00efdes dans le c\u0153ur et de nombreux autres organes. Le diagnostic est souvent retard\u00e9 car la maladie mime plusieurs ph\u00e9notypes cardiaques classiques (cardiomyopathie hypertrophique, insuffisance cardiaque \u00e0 FEVG pr\u00e9serv\u00e9e ou alt\u00e9r\u00e9e). Les manifestations extracardiaques \u2014 canal carpien, atteintes ORL, dysautonomie, neuropathie p\u00e9riph\u00e9rique, syndrome n\u00e9phrotique \u2014 constituent des signes d&rsquo;alerte pr\u00e9coces \u00e0 ne pas n\u00e9gliger. Face \u00e0 une suspicion, le m\u00e9decin g\u00e9n\u00e9raliste doit adresser rapidement le patient \u00e0 un centre expert du R\u00e9seau Amylose, la prise en charge \u00e9tant une urgence, en particulier pour l&rsquo;amylose AL, \u00e0 \u00e9volution rapide. Le Protocole National de Diagnostic et de Soins, \u00e9labor\u00e9 par le Centre de R\u00e9f\u00e9rence Amyloses Cardiaques (H\u00f4pital Henri-Mondor, APHP) selon la m\u00e9thodologie de la HAS, sert de r\u00e9f\u00e9rence pour la prise en charge.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-16e47fd elementor-widget elementor-widget-text-editor\" data-id=\"16e47fd\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li class=\"font-claude-response-body whitespace-normal break-words pl-2\"><strong>R\u00e9dig\u00e9 par<\/strong> : Contenu r\u00e9dig\u00e9 par l&rsquo;\u00e9quipe du Centre de r\u00e9f\u00e9rence des Amyloses Cardiaques<\/li><li class=\"font-claude-response-body whitespace-normal break-words pl-2\"><strong>Relu \/ valid\u00e9 par<\/strong> : Pr Thibaud DAMY, cardiologue, Coordonateur du CRAC Centre de R\u00e9f\u00e9rence des Amyloses Cardiaques APHP &#8211; CHU Henri-Mondor<\/li><li class=\"font-claude-response-body whitespace-normal break-words pl-2\"><strong>Date de derni\u00e8re mise \u00e0 jour<\/strong> 08\/2026<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<\/div>\n\t\t","protected":false},"excerpt":{"rendered":"<p>Pour le M\u00e9decin G\u00e9n\u00e9raliste Les amyloses cardiaques sont des maladies rares et syst\u00e9miques, entra\u00eenant le d\u00e9p\u00f4t de fibrilles amylo\u00efdes dans les organes atteints. Ces organes sont principalement le c\u0153ur, mais \u00e9galement les t\u00e9guments, les reins, le syst\u00e8me nerveux p\u00e9riph\u00e9rique et v\u00e9g\u00e9tatif, le tractus gastro-intestinal et le syst\u00e8me ORL. Cette maladie atteint quasi exclusivement les adultes. [&hellip;]<\/p>\n","protected":false},"author":2,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_acf_changed":false,"footnotes":""},"categories":[],"tags":[],"class_list":["post-5525","page","type-page","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v25.5 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Amylose cardiaque \u2014 Ce que le g\u00e9n\u00e9raliste doit savoir - R\u00e9seau Amylose<\/title>\n<meta name=\"description\" content=\"D\u00e9pistage, diagnostic, fragilit\u00e9 et prise en charge de l&#039;amylose cardiaque chez le sujet \u00e2g\u00e9 \u2014 le triple r\u00f4le du g\u00e9riatre.\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/reseau-amylose.org\/jesuissoignant\/pour-le-medecin-generaliste\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Amylose cardiaque \u2014 Ce que le g\u00e9n\u00e9raliste doit savoir - 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