{"id":3587,"date":"2021-04-14T12:30:51","date_gmt":"2021-04-14T12:30:51","guid":{"rendered":"https:\/\/www.reseau-amylose.org\/jesuissoignant\/?page_id=3587"},"modified":"2026-08-25T19:33:26","modified_gmt":"2026-08-25T17:33:26","slug":"les-traitements-des-atteintes-cardiaques-des-amyloses-al","status":"publish","type":"page","link":"https:\/\/reseau-amylose.org\/jesuissoignant\/les-traitements-des-atteintes-cardiaques-des-amyloses-al\/","title":{"rendered":"Les traitements des amyloses AL"},"content":{"rendered":"\t\t<div data-elementor-type=\"wp-page\" data-elementor-id=\"3587\" class=\"elementor elementor-3587\" data-elementor-post-type=\"page\">\n\t\t\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-d95a6e0 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"d95a6e0\" data-element_type=\"section\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-934bbcb\" data-id=\"934bbcb\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-438d110 elementor-widget elementor-widget-heading\" data-id=\"438d110\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h1 class=\"elementor-heading-title elementor-size-default\">Les traitements des amyloses AL<\/h1>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-2b92dd97 elementor-widget-divider--view-line elementor-widget elementor-widget-divider\" data-id=\"2b92dd97\" data-element_type=\"widget\" data-widget_type=\"divider.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-divider\">\n\t\t\t<span class=\"elementor-divider-separator\">\n\t\t\t\t\t\t<\/span>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-45bcf36c elementor-widget elementor-widget-heading\" data-id=\"45bcf36c\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h6 class=\"elementor-heading-title elementor-size-default\"><h2 class=\"elementor-heading-title elementor-size-large elementor-inline-editing pen\" data-elementor-setting-key=\"title\" data-pen-placeholder=\"\u00c9crivez ici...\">Les traitements de l'amylose<\/h2><\/h6>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-7d1fa8f elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"7d1fa8f\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-5ee68c7\" data-id=\"5ee68c7\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-a214008 elementor-widget elementor-widget-text-editor\" data-id=\"a214008\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><em>Le traitement de l&rsquo;amylose AL a beaucoup \u00e9volu\u00e9 gr\u00e2ce aux nouvelles chimioth\u00e9rapies et \u00e0 l&rsquo;immunoth\u00e9rapie, am\u00e9liorant consid\u00e9rablement le pronostic des patients. Une r\u00e9gression de l&rsquo;infiltration et une am\u00e9lioration des sympt\u00f4mes sont fr\u00e9quemment observ\u00e9es. La prise en charge des formes cardiaques avanc\u00e9es (stades IIIA et IIIB) repose sur une organisation multidisciplinaire r\u00e9gionale.<\/em><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-c15a202 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"c15a202\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-d5595b8\" data-id=\"d5595b8\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-875843e elementor-widget elementor-widget-heading\" data-id=\"875843e\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Points cl\u00e9s pour les professionnels de sant\u00e9<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-957daa9 elementor-widget elementor-widget-text-editor\" data-id=\"957daa9\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li>Les nouvelles chimioth\u00e9rapies et l&rsquo;immunoth\u00e9rapie ont consid\u00e9rablement am\u00e9lior\u00e9 le pronostic de l&rsquo;amylose AL, avec r\u00e9gression fr\u00e9quente de l&rsquo;infiltration.<\/li><li>La cytog\u00e9n\u00e9tique aide \u00e0 mieux orienter le traitement de l&rsquo;amylose AL.<\/li><li>La dexam\u00e9thasone et le daratumumab font partie des options th\u00e9rapeutiques discut\u00e9es, avec une attention port\u00e9e \u00e0 leurs cons\u00e9quences cardiaques.<\/li><li>Les stades avanc\u00e9s (IIIA et IIIB, classification European staging) n\u00e9cessitent une prise en charge multidisciplinaire, organis\u00e9e r\u00e9gionalement (Cr\u00e9teil, Lyon, Toulouse notamment).<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-59f51bc elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"59f51bc\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-528480d7\" data-id=\"528480d7\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-2509586 elementor-widget elementor-widget-heading\" data-id=\"2509586\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Traitement sp\u00e9cifique de l'amylose AL<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-661bd203 elementor-widget elementor-widget-text-editor\" data-id=\"661bd203\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Le traitement des amyloses AL a beaucoup \u00e9volu\u00e9 et l&rsquo;utilisation de nouvelles chimioth\u00e9rapies et de l&rsquo;immunoth\u00e9rapie a permis d&rsquo;am\u00e9liorer consid\u00e9rablement le pronostic des patients. Il est fr\u00e9quent d&rsquo;observer une r\u00e9gression de l&rsquo;infiltration et une am\u00e9lioration des sympt\u00f4mes.<\/p><p>Un compos\u00e9 du th\u00e9 vert (\u00e9pigallocat\u00e9chine-3-gallate, EGCG) a \u00e9galement montr\u00e9 son int\u00e9r\u00eat pour r\u00e9duire la masse ventriculaire mesur\u00e9e en \u00e9chocardiographie et en IRM, dans une \u00e9tude non randomis\u00e9e de faible effectif.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-4fc795d elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"4fc795d\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-d051ed9\" data-id=\"d051ed9\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap\">\n\t\t\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-7ac9e55\" data-id=\"7ac9e55\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-4c342fe elementor-widget elementor-widget-heading\" data-id=\"4c342fe\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Les traitements de l'amylose AL<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-92b76a5 elementor-widget elementor-widget-heading\" data-id=\"92b76a5\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">Pr Arnaud JACCARD<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-52e68c60 elementor-widget elementor-widget-video\" data-id=\"52e68c60\" data-element_type=\"widget\" data-settings=\"{&quot;youtube_url&quot;:&quot;https:\\\/\\\/www.youtube.com\\\/watch?v=ZDaZT4BKowM&amp;ab_channel=R%C3%A9seauAmylose&quot;,&quot;video_type&quot;:&quot;youtube&quot;,&quot;controls&quot;:&quot;yes&quot;}\" data-widget_type=\"video.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-wrapper elementor-open-inline\">\n\t\t\t<div class=\"elementor-video\"><\/div>\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-85edbd6\" data-id=\"85edbd6\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-2a9e56e elementor-widget elementor-widget-heading\" data-id=\"2a9e56e\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Comment utiliser la cytog\u00e9n\u00e9tique pour mieux traiter les amyloses AL<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-27b60ee elementor-widget elementor-widget-heading\" data-id=\"27b60ee\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">Dr Fabien LE BRAS<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-97d6685 elementor-widget elementor-widget-video\" data-id=\"97d6685\" data-element_type=\"widget\" data-settings=\"{&quot;youtube_url&quot;:&quot;https:\\\/\\\/www.youtube.com\\\/watch?v=kCPNbZ4diXQ&amp;ab_channel=R%C3%A9seauAmylose&quot;,&quot;video_type&quot;:&quot;youtube&quot;,&quot;controls&quot;:&quot;yes&quot;}\" data-widget_type=\"video.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-wrapper elementor-open-inline\">\n\t\t\t<div class=\"elementor-video\"><\/div>\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-47460acb elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"47460acb\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-21b1dc69\" data-id=\"21b1dc69\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-6015e8e elementor-widget elementor-widget-heading\" data-id=\"6015e8e\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Chimioth\u00e9rapies dans l'amylose AL : ce que le cardiologue doit savoir<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-a3c1140 elementor-widget elementor-widget-heading\" data-id=\"a3c1140\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">Pr Dania MOHTY<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-43156a44 elementor-widget elementor-widget-video\" data-id=\"43156a44\" data-element_type=\"widget\" data-settings=\"{&quot;youtube_url&quot;:&quot;https:\\\/\\\/www.youtube.com\\\/watch?v=qf-S3or2CBs&amp;ab_channel=R%C3%A9seauAmylose&quot;,&quot;video_type&quot;:&quot;youtube&quot;,&quot;controls&quot;:&quot;yes&quot;}\" data-widget_type=\"video.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-wrapper elementor-open-inline\">\n\t\t\t<div class=\"elementor-video\"><\/div>\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-6954bdb4\" data-id=\"6954bdb4\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-71a5804 elementor-widget elementor-widget-heading\" data-id=\"71a5804\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Chimioth\u00e9rapies dans les amyloses AL et impact pour le coeur<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-fb0c5d8 elementor-widget elementor-widget-heading\" data-id=\"fb0c5d8\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">Pr Thibaud DAMY<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-25fb3b54 elementor-widget elementor-widget-video\" data-id=\"25fb3b54\" data-element_type=\"widget\" data-settings=\"{&quot;youtube_url&quot;:&quot;https:\\\/\\\/www.youtube.com\\\/watch?v=IZuLpQ4x62M&amp;ab_channel=R%C3%A9seauAmylose&quot;,&quot;video_type&quot;:&quot;youtube&quot;,&quot;controls&quot;:&quot;yes&quot;}\" data-widget_type=\"video.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-wrapper elementor-open-inline\">\n\t\t\t<div class=\"elementor-video\"><\/div>\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-147bf4b9\" data-id=\"147bf4b9\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap\">\n\t\t\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-4a4f2b55 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"4a4f2b55\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-79255c9e\" data-id=\"79255c9e\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-dcc2417 elementor-widget elementor-widget-heading\" data-id=\"dcc2417\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Cons\u00e9quences cardiaques de la dexam\u00e9thasone dans l'amylose cardiaque AL<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-e59f6a0 elementor-widget elementor-widget-heading\" data-id=\"e59f6a0\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">Mme M\u00e9lanie BEZARD<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-43967af4 elementor-widget elementor-widget-video\" data-id=\"43967af4\" data-element_type=\"widget\" data-settings=\"{&quot;youtube_url&quot;:&quot;https:\\\/\\\/www.youtube.com\\\/watch?v=nyIScw4qumc&amp;ab_channel=R%C3%A9seauAmylose&quot;,&quot;video_type&quot;:&quot;youtube&quot;,&quot;controls&quot;:&quot;yes&quot;}\" data-widget_type=\"video.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-wrapper elementor-open-inline\">\n\t\t\t<div class=\"elementor-video\"><\/div>\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-49157630\" data-id=\"49157630\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-f526059 elementor-widget elementor-widget-heading\" data-id=\"f526059\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Int\u00e9r\u00eat de la dexam\u00e9thasone dans l'amylose AL<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-8803707 elementor-widget elementor-widget-heading\" data-id=\"8803707\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">Pr Arnaud JACCARD<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-22ab09ab elementor-widget elementor-widget-video\" data-id=\"22ab09ab\" data-element_type=\"widget\" data-settings=\"{&quot;youtube_url&quot;:&quot;https:\\\/\\\/www.youtube.com\\\/watch?v=fKDwz1FQvyc&amp;ab_channel=R%C3%A9seauAmylose&quot;,&quot;video_type&quot;:&quot;youtube&quot;,&quot;controls&quot;:&quot;yes&quot;}\" data-widget_type=\"video.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-wrapper elementor-open-inline\">\n\t\t\t<div class=\"elementor-video\"><\/div>\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-132beb37\" data-id=\"132beb37\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-af9a848 elementor-widget elementor-widget-heading\" data-id=\"af9a848\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Le Daratumumab pour traiter les amyloses AL<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-2484f3a elementor-widget elementor-widget-heading\" data-id=\"2484f3a\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">Dr Antoine HUART<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-360cb6cb elementor-widget elementor-widget-video\" data-id=\"360cb6cb\" data-element_type=\"widget\" data-settings=\"{&quot;youtube_url&quot;:&quot;https:\\\/\\\/www.youtube.com\\\/watch?v=XjWRv7EG3xY&amp;ab_channel=R%C3%A9seauAmylose&quot;,&quot;video_type&quot;:&quot;youtube&quot;,&quot;controls&quot;:&quot;yes&quot;}\" data-widget_type=\"video.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-wrapper elementor-open-inline\">\n\t\t\t<div class=\"elementor-video\"><\/div>\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-bc2d784 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"bc2d784\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-4fe8dc9\" data-id=\"4fe8dc9\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-7fe90fb elementor-widget elementor-widget-heading\" data-id=\"7fe90fb\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Les traitements des amyloses AL IIIA et IIIB - Partage des organisations r\u00e9gionales<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-46ff4af elementor-widget elementor-widget-text-editor\" data-id=\"46ff4af\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<h3><strong>Le parcours de soin des amyloses AL IIIA et IIIB <\/strong>(classification European staging).<\/h3><p>Les amyloses AL avec atteinte cardiaque doivent \u00eatre g\u00e9r\u00e9es de mani\u00e8re multidisciplinaire, avec h\u00e9matologues, cardiologues, n\u00e9phrologues, etc.<\/p><p>Dans chaque r\u00e9gion, les centres du R\u00e9seau Amylose se sont organis\u00e9s pour prendre en charge de mani\u00e8re multiprofessionnelle et interdisciplinaire les patients atteints d&rsquo;amylose cardiaque au stade IIIA ou IIIB.<\/p><p>Trois vid\u00e9os pr\u00e9sentent les organisations d\u00e9velopp\u00e9es par le CHU Henri-Mondor, le CHU de Rangueil (Toulouse) et les Hospices Civils de Lyon.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-e6cf4cb elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"e6cf4cb\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-e5a408f\" data-id=\"e5a408f\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-e2c064d elementor-widget elementor-widget-heading\" data-id=\"e2c064d\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">La prise en charge \u00e0 Lyon<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-73d4460 elementor-widget elementor-widget-heading\" data-id=\"73d4460\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">Dr Antoine JOBBE-DUVAL<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-8e8058a elementor-widget elementor-widget-video\" data-id=\"8e8058a\" data-element_type=\"widget\" data-settings=\"{&quot;youtube_url&quot;:&quot;https:\\\/\\\/www.youtube.com\\\/watch?v=x5uNdfV4Ucs&amp;list=PLgcbJqP0xnzhFqwERU2_B1ltwSIBhKV0t&amp;index=22&quot;,&quot;video_type&quot;:&quot;youtube&quot;,&quot;controls&quot;:&quot;yes&quot;}\" data-widget_type=\"video.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-wrapper elementor-open-inline\">\n\t\t\t<div class=\"elementor-video\"><\/div>\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-c0e8afb\" data-id=\"c0e8afb\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-e5996a4 elementor-widget elementor-widget-heading\" data-id=\"e5996a4\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">La prise en charge \u00e0 Toulouse<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-1cfc134 elementor-widget elementor-widget-heading\" data-id=\"1cfc134\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">Dr Eve CARIOU<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-817d04f elementor-widget elementor-widget-video\" data-id=\"817d04f\" data-element_type=\"widget\" data-settings=\"{&quot;youtube_url&quot;:&quot;https:\\\/\\\/www.youtube.com\\\/watch?v=e5ZaXyBqB4Y&amp;list=PLgcbJqP0xnzhFqwERU2_B1ltwSIBhKV0t&amp;index=23&quot;,&quot;video_type&quot;:&quot;youtube&quot;,&quot;controls&quot;:&quot;yes&quot;}\" data-widget_type=\"video.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-wrapper elementor-open-inline\">\n\t\t\t<div class=\"elementor-video\"><\/div>\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-5a493a6\" data-id=\"5a493a6\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-140a95b elementor-widget elementor-widget-heading\" data-id=\"140a95b\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">La prise en charge \u00e0 Cr\u00e9teil<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-46aba32 elementor-widget elementor-widget-heading\" data-id=\"46aba32\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">Dr Amira ZAROUI<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-22c98a4 elementor-widget elementor-widget-video\" data-id=\"22c98a4\" data-element_type=\"widget\" data-settings=\"{&quot;youtube_url&quot;:&quot;https:\\\/\\\/www.youtube.com\\\/watch?v=8tHNWEO1SdI&amp;list=PLgcbJqP0xnzhFqwERU2_B1ltwSIBhKV0t&amp;index=21&quot;,&quot;video_type&quot;:&quot;youtube&quot;,&quot;controls&quot;:&quot;yes&quot;}\" data-widget_type=\"video.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-wrapper elementor-open-inline\">\n\t\t\t<div class=\"elementor-video\"><\/div>\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-76134e6 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"76134e6\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-05b9a3e\" data-id=\"05b9a3e\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-ced622b elementor-widget elementor-widget-heading\" data-id=\"ced622b\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">FAQ \u2014 Questions fr\u00e9quentes<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-3cad9af elementor-widget elementor-widget-toggle\" data-id=\"3cad9af\" data-element_type=\"widget\" data-widget_type=\"toggle.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-toggle\">\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-6361\" class=\"elementor-tab-title\" data-tab=\"1\" role=\"button\" aria-controls=\"elementor-tab-content-6361\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-left\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Quels traitements ont transform\u00e9 le pronostic de l'amylose AL ?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-6361\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"1\" role=\"region\" aria-labelledby=\"elementor-tab-title-6361\"><p>Les nouvelles chimioth\u00e9rapies et l&rsquo;immunoth\u00e9rapie, qui permettent souvent une r\u00e9gression de l&rsquo;infiltration amylo\u00efde et une am\u00e9lioration des sympt\u00f4mes.<\/p><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-6362\" class=\"elementor-tab-title\" data-tab=\"2\" role=\"button\" aria-controls=\"elementor-tab-content-6362\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-left\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Comment sont pris en charge les patients au stade IIIA\/IIIB de l'amylose AL ?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-6362\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"2\" role=\"region\" aria-labelledby=\"elementor-tab-title-6362\"><p>Par une organisation multidisciplinaire r\u00e9gionale associant h\u00e9matologues, cardiologues et n\u00e9phrologues, structur\u00e9e diff\u00e9remment selon les centres du R\u00e9seau Amylose (Cr\u00e9teil, Lyon, Toulouse).<\/p><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-6363\" class=\"elementor-tab-title\" data-tab=\"3\" role=\"button\" aria-controls=\"elementor-tab-content-6363\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-left\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Le th\u00e9 vert (EGCG) a-t-il un int\u00e9r\u00eat d\u00e9montr\u00e9 dans l'amylose AL ?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-6363\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"3\" role=\"region\" aria-labelledby=\"elementor-tab-title-6363\"><p>Une \u00e9tude non randomis\u00e9e de faible effectif a montr\u00e9 un int\u00e9r\u00eat pour r\u00e9duire la masse ventriculaire en \u00e9chocardiographie et en IRM, mais ce n&rsquo;est pas un traitement de r\u00e9f\u00e9rence valid\u00e9 \u00e0 large \u00e9chelle.<\/p><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-4cb8e556 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"4cb8e556\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-49c18300\" data-id=\"49c18300\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-c1e948d elementor-widget elementor-widget-text-editor\" data-id=\"c1e948d\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<div id=\"elementor-tab-content-1336\" class=\"elementor-tab-content elementor-clearfix elementor-active\" role=\"tabpanel\" data-tab=\"6\" aria-labelledby=\"elementor-tab-title-1336\"><h5><span style=\"color: #4db8f0\"><strong>R\u00e9f\u00e9rences<\/strong><\/span><\/h5><h5>1. <a href=\"http:\/\/www.ncbi.nlm.nih.gov\/pubmed\/?term=Molecular+Mechanisms+of+Amyloidosis.+Merlini+G.+and+Bellotti+V.N+Engl+Med+2003%3B349%3A583-96\" target=\"_blank\" rel=\"noopener\">Molecular Mechanisms of Amyloidosis. Merlini G. and Bellotti V.N Engl Med 2003;349:583-96<\/a><\/h5><h5>2. <a href=\"http:\/\/www.ncbi.nlm.nih.gov\/pubmed\/?term=Familial+amyloid+polyneuropathy+A+clinico-pathologic+study.+Said+G%2C+Plant%C3%A9-Bordeneuve+V.+Journal+of+the+Neurological+Sciences+284+(2009)+149%E2%80%93154.\" target=\"_blank\" rel=\"noopener\">Familial amyloid polyneuropathy A clinico-pathologic study. Said G, Plant\u00e9-Bordeneuve V. Journal of the Neurological Sciences 284 (2009) 149\u2013154.<\/a><\/h5><h5>3. <a href=\"http:\/\/www.ncbi.nlm.nih.gov\/pubmed\/?term=Variant-sequence+transthyretin+(isoleucine+122)+in+late-onset+cardiac+amyloidosis+in+black+Americans.+Jacobson+DR%2C+Pastore+RD%2C+Yaghoubian+R%2C+Kane+I%2C+Gallo+G%2C+Buck+FS%2CBuxbaum+JN.+N+Engl+J+Med+1997%3B336%3A466%E2%80%93473.\" target=\"_blank\" rel=\"noopener\">Variant-sequence transthyretin (isoleucine 122) in late-onset cardiac amyloidosis in black Americans. Jacobson DR, Pastore RD, Yaghoubian R, Kane I, Gallo G, Buck FS,Buxbaum JN. N Engl J Med 1997;336:466\u2013473.<\/a><\/h5><h5>4. <a href=\"http:\/\/www.ncbi.nlm.nih.gov\/pubmed\/?term=Relative+apical+sparing+of+longitudinal+strain+using+two-dimensional+speckle-tracking+echocardiography+is+both+sensitive+and+specific+for+the+diagnosis+of+cardiac+amyloidosis.+Dermot+Phelan%2C+Collier+P%2C+Popovi%C4%87+Z%2CHanna+M%2C+Plana+JC%2C+Marwick+TH%2C+Thomas+JD.++Heart+2012%3B98%3A1442-1448.\" target=\"_blank\" rel=\"noopener\">Relative apical sparing of longitudinal strain using two-dimensional speckle-tracking echocardiography is both sensitive and specific for the diagnosis of cardiac amyloidosis. Dermot Phelan, Collier P,\u00a0Popovi\u0107 Z,Hanna M,\u00a0Plana JC, Marwick TH,\u00a0Thomas JD. \u00a0Heart\u00a02012;98:1442-1448.<\/a><\/h5><h5>5. <a href=\"http:\/\/www.ncbi.nlm.nih.gov\/pubmed\/?term=Non-invasive+evaluation+of+the+myocardial+substrate+of+cardiac+amyloidosis+by+gadolinium+cardiac+magnetic+resonance.+Perugini+E%2C+Rapezzi+C%2C+Piva+T%2C+Leone+O%2C+Bacchi-Reggiani+L%2C+Riva+L%2C+Salvi+F%2C+Lovato+L%2C+Branzi+A%2C+Fattori+R.+Heart.+2006+Mar%3B92(3)%3A343-9.\" target=\"_blank\" rel=\"noopener\">Non-invasive evaluation of the myocardial substrate of cardiac amyloidosis by gadolinium cardiac magnetic resonance. Perugini E,\u00a0Rapezzi C,\u00a0Piva T,\u00a0Leone O,\u00a0Bacchi-Reggiani L,\u00a0Riva L,\u00a0Salvi F,\u00a0Lovato L,\u00a0Branzi A,\u00a0Fattori R. Heart.\u00a02006 Mar;92(3):343-9.<\/a><\/h5><h5>6. <a href=\"http:\/\/www.ncbi.nlm.nih.gov\/pubmed\/?term=Intracardiac+thrombosis+and+embolism+in+patients+with+cardiac+amyloidosis.+Feng+D%2C+Edwards+WD%2C+Oh+JK%2C+Chandrasekaran+K%2C+Grogan+M%2C+Martinez+MW%2C+Syed+IS%2C+Hughes+DA%2C+Lust+JA%2C+Jaffe+AS%2C+Gertz+MA%2C+Klarich+KW.+Circulation+2007%3B116%3A2420%E2%80%932426.\" target=\"_blank\" rel=\"noopener\">Intracardiac thrombosis and embolism in patients with cardiac amyloidosis. Feng D, Edwards WD, Oh JK, Chandrasekaran K, Grogan M, Martinez MW, Syed IS, Hughes DA, Lust JA, Jaffe AS, Gertz MA, Klarich KW. Circulation 2007;116:2420\u20132426.<\/a><\/h5><h5>7. <a href=\"http:\/\/www.ncbi.nlm.nih.gov\/pubmed\/?term=Intracardiac+thrombosis+and+embolism+in+patients+with+cardiac+amyloidosis.+Feng+D%2C+Edwards+WD%2C+Oh+JK%2C+Chandrasekaran+K%2C+Grogan+M%2C+Martinez+MW%2C+Syed+IS%2C+Hughes+DA%2C+Lust+JA%2C+Jaffe+AS%2C+Gertz+MA%2C+Klarich+KW.+Circulation+2007%3B116%3A2420%E2%80%932426.\">Role of (99m)Tc-DPD scintigraphy in diagnosis and prognosis of hereditary transthyretin-related cardiac amyloidosis. Rapezzi C, Quarta CC, Guidalotti PL, Pettinato C, Fanti S, Leone O, Ferlini A, Longhi S, Lorenzini M, Reggiani LB, Gagliardi C, Gallo P, Villani C, Salvi F. JACC Cardiovasc Imaging. 2011 Jun;4(6):659-70. <\/a><\/h5><\/div>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-510cb3ac elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"510cb3ac\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-1c773485\" data-id=\"1c773485\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-470736d elementor-widget elementor-widget-text-editor\" data-id=\"470736d\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Le traitement de l&rsquo;amylose AL repose sur la chimioth\u00e9rapie et l&rsquo;immunoth\u00e9rapie, qui ont consid\u00e9rablement am\u00e9lior\u00e9 le pronostic des patients, avec des r\u00e9gressions fr\u00e9quentes de l&rsquo;infiltration amylo\u00efde. La cytog\u00e9n\u00e9tique aide \u00e0 orienter le choix th\u00e9rapeutique, et des mol\u00e9cules comme la dexam\u00e9thasone ou le daratumumab font partie de l&rsquo;arsenal disponible. Pour les formes cardiaques avanc\u00e9es (stades IIIA et IIIB selon la classification European staging), une prise en charge multidisciplinaire est indispensable ; le R\u00e9seau Amylose a structur\u00e9 des organisations r\u00e9gionales d\u00e9di\u00e9es, notamment \u00e0 Cr\u00e9teil, Lyon et Toulouse, pour coordonner h\u00e9matologues, cardiologues et n\u00e9phrologues autour de ces patients.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-3313189 elementor-widget elementor-widget-text-editor\" data-id=\"3313189\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li class=\"font-claude-response-body whitespace-normal break-words pl-2\"><strong>R\u00e9dig\u00e9 par<\/strong> : Contenu r\u00e9dig\u00e9 par l&rsquo;\u00e9quipe du Centre de r\u00e9f\u00e9rence des Amyloses Cardiaques<\/li><li class=\"font-claude-response-body whitespace-normal break-words pl-2\"><strong>Relu \/ valid\u00e9 par<\/strong> : Pr Thibaud DAMY, cardiologue, Coordonateur du CRAC Centre de R\u00e9f\u00e9rence des Amyloses Cardiaques APHP &#8211; CHU Henri-Mondor<\/li><li class=\"font-claude-response-body whitespace-normal break-words pl-2\"><strong>Date de derni\u00e8re mise \u00e0 jour<\/strong> 08\/2026<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-3706f060 elementor-widget elementor-widget-spacer\" data-id=\"3706f060\" data-element_type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<\/div>\n\t\t","protected":false},"excerpt":{"rendered":"<p>Les traitements des amyloses AL Les traitements de l&rsquo;amylose Le traitement de l&rsquo;amylose AL a beaucoup \u00e9volu\u00e9 gr\u00e2ce aux nouvelles chimioth\u00e9rapies et \u00e0 l&rsquo;immunoth\u00e9rapie, am\u00e9liorant consid\u00e9rablement le pronostic des patients. Une r\u00e9gression de l&rsquo;infiltration et une am\u00e9lioration des sympt\u00f4mes sont fr\u00e9quemment observ\u00e9es. La prise en charge des formes cardiaques avanc\u00e9es (stades IIIA et IIIB) repose [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_acf_changed":false,"footnotes":""},"categories":[],"tags":[],"class_list":["post-3587","page","type-page","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v25.5 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Traitements de l&#039;amylose cardiaque AL - R\u00e9seau Amylose<\/title>\n<meta name=\"description\" content=\"Chimioth\u00e9rapie, immunoth\u00e9rapie, cytog\u00e9n\u00e9tique : les traitements sp\u00e9cifiques de l&#039;amylose AL et l&#039;organisation des fili\u00e8res r\u00e9gionales.\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/reseau-amylose.org\/jesuissoignant\/les-traitements-des-atteintes-cardiaques-des-amyloses-al\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Traitements de l&#039;amylose cardiaque AL - R\u00e9seau Amylose\" \/>\n<meta property=\"og:description\" content=\"Chimioth\u00e9rapie, immunoth\u00e9rapie, cytog\u00e9n\u00e9tique : les traitements sp\u00e9cifiques de l&#039;amylose AL et l&#039;organisation des fili\u00e8res r\u00e9gionales.\" \/>\n<meta property=\"og:url\" content=\"https:\/\/reseau-amylose.org\/jesuissoignant\/les-traitements-des-atteintes-cardiaques-des-amyloses-al\/\" \/>\n<meta property=\"og:site_name\" content=\"R\u00e9seau Amylose\" \/>\n<meta property=\"article:modified_time\" content=\"2026-08-25T17:33:26+00:00\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Dur\u00e9e de lecture estim\u00e9e\" \/>\n\t<meta name=\"twitter:data1\" content=\"5 minutes\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\/\/schema.org\",\"@graph\":[{\"@type\":\"WebPage\",\"@id\":\"https:\/\/reseau-amylose.org\/jesuissoignant\/les-traitements-des-atteintes-cardiaques-des-amyloses-al\/\",\"url\":\"https:\/\/reseau-amylose.org\/jesuissoignant\/les-traitements-des-atteintes-cardiaques-des-amyloses-al\/\",\"name\":\"Traitements de l'amylose cardiaque AL - 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