{"id":2827,"date":"2021-02-19T08:26:05","date_gmt":"2021-02-19T08:26:05","guid":{"rendered":"https:\/\/www.reseau-amylose.org\/jesuissoignant\/?page_id=2827"},"modified":"2026-08-22T10:56:19","modified_gmt":"2026-08-22T08:56:19","slug":"pour-le-geriatre","status":"publish","type":"page","link":"https:\/\/reseau-amylose.org\/jesuissoignant\/pour-le-geriatre\/","title":{"rendered":"Pour le G\u00e9riatre"},"content":{"rendered":"\t\t<div data-elementor-type=\"wp-page\" data-elementor-id=\"2827\" class=\"elementor elementor-2827\" data-elementor-post-type=\"page\">\n\t\t\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-51a567e5 elementor-section-content-middle elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"51a567e5\" data-element_type=\"section\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-no\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-2639c392\" data-id=\"2639c392\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-138e180 elementor-widget elementor-widget-heading\" data-id=\"138e180\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h1 class=\"elementor-heading-title elementor-size-default\">Pour le G\u00e9riatre<\/h1>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-45060b86 elementor-widget-divider--view-line elementor-widget elementor-widget-divider\" data-id=\"45060b86\" data-element_type=\"widget\" data-widget_type=\"divider.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-divider\">\n\t\t\t<span class=\"elementor-divider-separator\">\n\t\t\t\t\t\t<\/span>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-fa2f994 elementor-widget elementor-widget-heading\" data-id=\"fa2f994\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">D\u00e9pister, diagnostiquer et prendre en charge les amylose cardiaques<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-bd9b3a6 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"bd9b3a6\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-13bf668\" data-id=\"13bf668\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-054749f elementor-widget elementor-widget-heading\" data-id=\"054749f\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Points cl\u00e9s pour les professionnels de sant\u00e9<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-7814c5b elementor-widget elementor-widget-text-editor\" data-id=\"7814c5b\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li>15 \u00e0 20 % des patients \u00e2g\u00e9s hospitalis\u00e9s pour insuffisance cardiaque \u00e0 FEVG pr\u00e9serv\u00e9e ont potentiellement une amylose cardiaque sous-jacente.<\/li><li>Trois manifestations doivent alerter : cardiaques (IC r\u00e9sistante, microvoltage paradoxal), ost\u00e9o-articulaires (canal carpien, Dupuytren, canal lombaire) et neurosensorielles (neuropathie, macroglossie, dysautonomie).<\/li><li>Le score SEGA (fragile si &gt; 8) et l&rsquo;EGA multidimensionnelle sont les outils de d\u00e9pistage et d&rsquo;\u00e9valuation de la fragilit\u00e9.<\/li><li>La fragilit\u00e9 touche la grande majorit\u00e9 des patients \u00e2g\u00e9s amylo\u00efdes : perte d&rsquo;autonomie (69 %), syndrome dysex\u00e9cutif (72 %), faiblesse musculaire (74 %).<\/li><li>Le triple r\u00f4le du g\u00e9riatre : d\u00e9pister\/diagnostiquer, orienter vers un centre de r\u00e9f\u00e9rence, \u00e9valuer la fragilit\u00e9 pour optimiser la prise en charge.<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-16c0f32 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"16c0f32\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-b278219\" data-id=\"b278219\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-e8bd4d7 elementor-widget elementor-widget-heading\" data-id=\"e8bd4d7\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Insuffisance cardiaque et amylose\u00a0<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-14be216 elementor-widget elementor-widget-text-editor\" data-id=\"14be216\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>L&rsquo;insuffisance cardiaque (IC) est le premier motif d&rsquo;hospitalisation en Unit\u00e9 de G\u00e9riatrie Aigu\u00eb. Les g\u00e9riatres sont donc en premi\u00e8re ligne avec les cardiologues dans la prise en charge de l&rsquo;insuffisance cardiaque du sujet \u00e2g\u00e9. L&rsquo;IC \u00e0 fraction d&rsquo;\u00e9jection pr\u00e9serv\u00e9e est la forme la plus fr\u00e9quente dans cette population. Parmi ces patients, 15 \u00e0 20 % ont peut-\u00eatre une amylose cardiaque.<\/p><p>Les amyloses cardiaques (AC) sont sous-diagnostiqu\u00e9es. Il s&rsquo;agit de maladies syst\u00e9miques caract\u00e9ris\u00e9es par l&rsquo;accumulation de prot\u00e9ines sous forme de \u00ab fibrilles amylo\u00efdes \u00bb dans diff\u00e9rents organes tels que le c\u0153ur, le rein, le foie, le syst\u00e8me gastro-intestinal et nerveux, provoquant l&rsquo;alt\u00e9ration structurelle et la dysfonction des organes atteints.<\/p><p><strong>Les principaux types d&rsquo;AC atteignant le c\u0153ur du sujet \u00e2g\u00e9 sont :<\/strong><\/p><ul><li>L&rsquo;amylose \u00e0 transthyr\u00e9tine (ATTR) sauvage, aussi appel\u00e9e \u00ab s\u00e9nile \u00bb (ATTRwt pour wild-type).<\/li><li>L&rsquo;amylose \u00e0 transthyr\u00e9tine (ATTR) \u00ab h\u00e9r\u00e9ditaire \u00bb, aussi appel\u00e9e \u00ab mut\u00e9e \u00bb (ATTRv pour variant).<\/li><li>L&rsquo;amylose AL (maladie h\u00e9matologique).<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-985f170 elementor-widget elementor-widget-image\" data-id=\"985f170\" data-element_type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t<figure class=\"wp-caption\">\n\t\t\t\t\t\t\t\t\t\t<img fetchpriority=\"high\" decoding=\"async\" width=\"491\" height=\"224\" src=\"https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2021\/05\/CMH.png\" class=\"attachment-medium_large size-medium_large wp-image-4049\" alt=\"\" srcset=\"https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2021\/05\/CMH.png 491w, https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2021\/05\/CMH-300x137.png 300w\" sizes=\"(max-width: 491px) 100vw, 491px\" \/>\t\t\t\t\t\t\t\t\t\t\t<figcaption class=\"widget-image-caption wp-caption-text\">Figure : Cardiomyopathie hypertrophique<\/figcaption>\n\t\t\t\t\t\t\t\t\t\t<\/figure>\n\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-b4c49f8 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"b4c49f8\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-1931ef0\" data-id=\"1931ef0\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-d286297 elementor-widget elementor-widget-heading\" data-id=\"d286297\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Le diagnostic : quand y penser ?\u00a0<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-a4bbae1 elementor-widget elementor-widget-text-editor\" data-id=\"a4bbae1\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Les signes cliniques d\u00e9pendent des organes touch\u00e9s.<\/p><p><strong>Manifestations cardiaques :<\/strong><\/p><ul><li>Insuffisance cardiaque \u00e0 FEVG pr\u00e9serv\u00e9e avec hypertrophie ventriculaire gauche concentrique retrouv\u00e9e \u00e0 l&rsquo;ETT.<\/li><li>R\u00e9sistance aux traitements habituels de l&rsquo;IC, avec pouss\u00e9es it\u00e9ratives.<\/li><li>Microvoltage paradoxal \u00e0 l&rsquo;ECG.<\/li><\/ul><p><strong>Manifestations ost\u00e9o-articulaires :<\/strong><\/p><ul><li>Syndrome du canal carpien++.<\/li><li>Syndrome de Dupuytren.<\/li><li>Syndrome du canal lombaire \u00e9troit.<\/li><li>Rupture du tendon de l&rsquo;\u00e9paule et\/ou du biceps.<\/li><li>L\u00e9sions ungu\u00e9ales.<\/li><\/ul><p><strong>Manifestations neurosensorielles :<\/strong><\/p><ul><li>Neuropathie des extr\u00e9mit\u00e9s.<\/li><li>\u00a0<\/li><li>Dysautonomie (diarrh\u00e9es, vomissements).<\/li><li>Hypotension orthostatique.<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-7b41e38 elementor-widget elementor-widget-image\" data-id=\"7b41e38\" data-element_type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t<figure class=\"wp-caption\">\n\t\t\t\t\t\t\t\t\t\t<img decoding=\"async\" width=\"518\" height=\"312\" src=\"https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2021\/05\/atteintes-cardq-extracdq.png\" class=\"attachment-medium_large size-medium_large wp-image-4060\" alt=\"\" srcset=\"https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2021\/05\/atteintes-cardq-extracdq.png 518w, https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2021\/05\/atteintes-cardq-extracdq-300x181.png 300w\" sizes=\"(max-width: 518px) 100vw, 518px\" \/>\t\t\t\t\t\t\t\t\t\t\t<figcaption class=\"widget-image-caption wp-caption-text\">Figure : Atteintes cardiaques et extracardiaques<\/figcaption>\n\t\t\t\t\t\t\t\t\t\t<\/figure>\n\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-726fea5 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"726fea5\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-c99f98d\" data-id=\"c99f98d\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-2027046 elementor-widget elementor-widget-heading\" data-id=\"2027046\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Amylose et fragilit\u00e9<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-bce01e0 elementor-widget elementor-widget-text-editor\" data-id=\"bce01e0\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><strong>Les cons\u00e9quences des amyloses cardiaques pour les patients \u00e2g\u00e9s :<\/strong><\/p><ul><li>Autonomie : 69 % des patients en perte d&rsquo;ind\u00e9pendance fonctionnelle.<\/li><li>Neuro-cognitives : syndrome dysex\u00e9cutif (72 %).<\/li><li>Thymiques : syndrome d\u00e9pressif (49 %).<\/li><li>Motrices : faiblesse musculaire (74 %), troubles de la marche et de l&rsquo;\u00e9quilibre (58 %), s\u00e9dentarit\u00e9 (47 %), risque de chute (42 %) et sarcop\u00e9nie.<\/li><li>Nutritionnelles : anorexie, amaigrissement (31 %), malnutrition (39 %).<\/li><li>Troubles v\u00e9sico-sphinct\u00e9riens : incontinence urinaire par hyperactivit\u00e9 v\u00e9sicale.<\/li><li>Asth\u00e9nie (61 %).<\/li><\/ul><p><strong>Les tests utilis\u00e9s pour l&rsquo;\u00e9valuation globale et le d\u00e9pistage de la fragilit\u00e9 dans le cadre de l&rsquo;amylose cardiaque :<\/strong><\/p><ul><li>Le score Short Emergency Geriatric Assessment (SEGA) pour le d\u00e9pistage de la fragilit\u00e9 (non fragile : score \u2264 8 ; fragile et tr\u00e8s fragile : score &gt; 8).<\/li><li>Les \u00e9chelles ADL et IADL pour \u00e9valuer l&rsquo;autonomie.<\/li><li>Un bilan de d\u00e9brouillage cognitif : Mini-Mental State Examination (MMSE) et \u00e9valuation des fonctions ex\u00e9cutives (BREF et test de l&rsquo;Horloge).<\/li><li>\u00c9valuation de la d\u00e9pression avec l&rsquo;\u00e9chelle Geriatric Depression Scale (GDS ou mini-GDS).<\/li><li>\u00c9valuation de la performance physique, de l&rsquo;\u00e9quilibre et de la force musculaire par le Short Physical Performance Battery (SPPB).<\/li><li>Le Mini Nutritional Assessment (MNA) pour \u00e9valuer l&rsquo;\u00e9tat nutritionnel.<\/li><li>\u00c9valuation des fonctions v\u00e9sico-sphinct\u00e9riennes par l&rsquo;Urinary Symptom Profile (USP).<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-057f8b0 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"057f8b0\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-593dc80\" data-id=\"593dc80\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-e0a6fd9 elementor-widget elementor-widget-heading\" data-id=\"e0a6fd9\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">L'avis du g\u00e9riatre : le sujet \u00e2g\u00e9 - amylose et fragilit\u00e9<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-208f287 elementor-widget elementor-widget-heading\" data-id=\"208f287\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Dr Amaury BROUSSIER - g\u00e9riatre<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-44a1e08\" data-id=\"44a1e08\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-c776b79 elementor-widget elementor-widget-video\" data-id=\"c776b79\" data-element_type=\"widget\" data-settings=\"{&quot;youtube_url&quot;:&quot;https:\\\/\\\/youtu.be\\\/3KgoYqqhMO4&quot;,&quot;video_type&quot;:&quot;youtube&quot;,&quot;controls&quot;:&quot;yes&quot;}\" data-widget_type=\"video.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-wrapper elementor-open-inline\">\n\t\t\t<div class=\"elementor-video\"><\/div>\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-173904c elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"173904c\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-27ddca5\" data-id=\"27ddca5\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-62d2253 elementor-widget elementor-widget-heading\" data-id=\"62d2253\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Bilan de l'amylose<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-ca3171f elementor-widget elementor-widget-text-editor\" data-id=\"ca3171f\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><strong>Les examens \u00e0 demander en 1\u00e8re intention devant une suspicion d&rsquo;amylose cardiaque :<\/strong><\/p><p><strong>Bilan biologique : <\/strong>biomarqueurs (NT-proBNP et troponine ultrasensible), EPP, immunofixation et dosage des cha\u00eenes l\u00e9g\u00e8res libres, recherche de prot\u00e9inurie de Bence Jones, bilan h\u00e9patique et r\u00e9nal.<\/p><p><strong>ECG : <\/strong>microvoltage, troubles conductifs, fibrillation auriculaire ou flutter.<\/p><p><strong>\u00c9chocardiographie (examen central pour \u00e9voquer le diagnostic) : <\/strong>hypertrophie ventriculaire gauche circonf\u00e9rentielle, alt\u00e9ration typique du strain (alt\u00e9r\u00e9 \u00e0 la base du VG, pr\u00e9serv\u00e9 \u00e0 l&rsquo;apex du VG), insuffisance cardiaque \u00e0 FEVG pr\u00e9serv\u00e9e.<\/p><p>\u00a0<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-8e0f7c5 elementor-widget elementor-widget-image\" data-id=\"8e0f7c5\" data-element_type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img decoding=\"async\" width=\"768\" height=\"249\" src=\"https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2021\/05\/Capture-de\u0301cran-2021-05-20-a\u0300-11.11.52-768x249.png\" class=\"attachment-medium_large size-medium_large wp-image-4068\" alt=\"\" srcset=\"https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2021\/05\/Capture-de\u0301cran-2021-05-20-a\u0300-11.11.52-768x249.png 768w, https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2021\/05\/Capture-de\u0301cran-2021-05-20-a\u0300-11.11.52-300x97.png 300w, https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2021\/05\/Capture-de\u0301cran-2021-05-20-a\u0300-11.11.52-1024x332.png 1024w, https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2021\/05\/Capture-de\u0301cran-2021-05-20-a\u0300-11.11.52.png 1270w\" sizes=\"(max-width: 768px) 100vw, 768px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-d919e33 elementor-widget elementor-widget-text-editor\" data-id=\"d919e33\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<h6>Le bilan pourra \u00eatre compl\u00e9t\u00e9 en milieu sp\u00e9cialis\u00e9 par une scintigraphie osseuse aux bisphosphonates, une IRM cardiaque, et \u00e9ventuellement la r\u00e9alisation d&rsquo;une biopsie permettant de confirmer histologiquement l&rsquo;amylose. Il faut ensuite faire une analyse g\u00e9n\u00e9tique pour diff\u00e9rencier les formes d&rsquo;amylose TTR (int\u00e9r\u00eat du d\u00e9pistage familial). Le diagnostic de l&rsquo;amylose cardiaque repose donc sur des examens non invasifs et le recours \u00e0 un centre expert dans l&rsquo;amylose cardiaque.<\/h6>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-732acb0 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"732acb0\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-09346c6\" data-id=\"09346c6\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-ed2d0e7 elementor-widget elementor-widget-heading\" data-id=\"ed2d0e7\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Prise en charge<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-46c07a7 elementor-widget elementor-widget-text-editor\" data-id=\"46c07a7\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Elle se fait en collaboration avec les services de r\u00e9f\u00e9rence des maladies rares sp\u00e9cialis\u00e9s dans l&rsquo;amylose. Arr\u00eat des b\u00e9tabloquants, adaptation des doses des inhibiteurs du SRAA et, en fonction du type, du stade de la maladie et du pronostic, proposition d&rsquo;un traitement sp\u00e9cifique :<\/p><p><strong>Amylose TTR : <\/strong>le tafamidis est actuellement utilis\u00e9 pour stabiliser la transthyr\u00e9tine pathologique et ainsi emp\u00eacher son d\u00e9p\u00f4t (traitement bien tol\u00e9r\u00e9, en prise orale). Ce traitement ne permet pas d&rsquo;\u00e9liminer les d\u00e9p\u00f4ts d\u00e9j\u00e0 constitu\u00e9s, d&rsquo;o\u00f9 l&rsquo;int\u00e9r\u00eat de poser un diagnostic pr\u00e9cocement.<\/p><p><strong>Amylose AL : <\/strong>un programme de chimioth\u00e9rapie adapt\u00e9.<\/p><p>Une \u00e9valuation g\u00e9riatrique avec d\u00e9pistage de la fragilit\u00e9 permet d&rsquo;argumenter la prise en charge et d&rsquo;apporter une aide dans la d\u00e9cision th\u00e9rapeutique (pour le tafamidis : l&rsquo;am\u00e9lioration clinique n&rsquo;est observ\u00e9e qu&rsquo;au-del\u00e0 de 18 mois de traitement).<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-e68dde8 elementor-widget elementor-widget-text-editor\" data-id=\"e68dde8\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><strong>Le triple r\u00f4le du g\u00e9riatre dans la prise en charge de l&rsquo;amylose cardiaque du sujet \u00e2g\u00e9 :<\/strong><\/p><p><strong>\u00a0 \u00a0 \u00a01.<\/strong> D\u00e9pister et diagnostiquer.<\/p><p><strong>\u00a0 \u00a0 \u00a02.<\/strong> Orienter vers le centre de r\u00e9f\u00e9rence.<\/p><p><strong>\u00a0 \u00a0 \u00a03.<\/strong> \u00c9valuer la fragilit\u00e9 des patients pour optimiser leur prise en charge.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-008328e elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"008328e\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-25 elementor-top-column elementor-element elementor-element-aa2e1f1\" data-id=\"aa2e1f1\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap\">\n\t\t\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-3b1fdf2\" data-id=\"3b1fdf2\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-f558866 elementor-align-center elementor-widget elementor-widget-button\" data-id=\"f558866\" data-element_type=\"widget\" data-widget_type=\"button.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<div class=\"elementor-button-wrapper\">\n\t\t\t\t\t<a class=\"elementor-button elementor-button-link elementor-size-md\" href=\"https:\/\/reseau-amylose.org\/jesuissoignant\/documentation\/documentation-triptyques-reseau-amylose\/\" target=\"_blank\">\n\t\t\t\t\t\t<span class=\"elementor-button-content-wrapper\">\n\t\t\t\t\t\t\t\t\t<span class=\"elementor-button-text\">T\u00e9l\u00e9chargez le triptyque - D\u00e9pister l'amylose cardiaque chez le patient \u00e2g\u00e9<\/span>\n\t\t\t\t\t<\/span>\n\t\t\t\t\t<\/a>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-25 elementor-top-column elementor-element elementor-element-fc2ec2d\" data-id=\"fc2ec2d\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap\">\n\t\t\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-d5b5320 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"d5b5320\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-1be4540\" data-id=\"1be4540\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-297009b elementor-widget elementor-widget-heading\" data-id=\"297009b\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">FAQ \u2014 Questions fr\u00e9quentes<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-b0db476 elementor-widget elementor-widget-toggle\" data-id=\"b0db476\" data-element_type=\"widget\" data-widget_type=\"toggle.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-toggle\">\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1851\" class=\"elementor-tab-title\" data-tab=\"1\" role=\"button\" aria-controls=\"elementor-tab-content-1851\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-left\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Quelle proportion de patients \u00e2g\u00e9s insuffisants cardiaques a une amylose cardiaque ?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1851\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"1\" role=\"region\" aria-labelledby=\"elementor-tab-title-1851\"><p>Environ 15 \u00e0 20 % des patients \u00e2g\u00e9s hospitalis\u00e9s pour insuffisance cardiaque \u00e0 fraction d&rsquo;\u00e9jection pr\u00e9serv\u00e9e.<\/p><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1852\" class=\"elementor-tab-title\" data-tab=\"2\" role=\"button\" aria-controls=\"elementor-tab-content-1852\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-left\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Quel outil utiliser pour d\u00e9pister la fragilit\u00e9 chez un patient amylose ?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1852\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"2\" role=\"region\" aria-labelledby=\"elementor-tab-title-1852\"><p>Le score SEGA (Short Emergency Geriatric Assessment) : un score sup\u00e9rieur \u00e0 8 signe une fragilit\u00e9 ou une fragilit\u00e9 s\u00e9v\u00e8re, \u00e0 compl\u00e9ter par une \u00e9valuation g\u00e9riatrique approfondie.<\/p><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1853\" class=\"elementor-tab-title\" data-tab=\"3\" role=\"button\" aria-controls=\"elementor-tab-content-1853\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-left\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Quel est le traitement sp\u00e9cifique de l'amylose TTR chez le sujet \u00e2g\u00e9 ?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1853\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"3\" role=\"region\" aria-labelledby=\"elementor-tab-title-1853\"><p>Le tafamidis, qui stabilise la transthyr\u00e9tine pathologique et emp\u00eache son d\u00e9p\u00f4t, sans \u00e9liminer les d\u00e9p\u00f4ts d\u00e9j\u00e0 constitu\u00e9s d&rsquo;o\u00f9 l&rsquo;importance d&rsquo;un diagnostic pr\u00e9coce. L&rsquo;am\u00e9lioration clinique n&rsquo;est observ\u00e9e qu&rsquo;au-del\u00e0 de 18 mois de traitement.<\/p><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1854\" class=\"elementor-tab-title\" data-tab=\"4\" role=\"button\" aria-controls=\"elementor-tab-content-1854\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-left\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Quel est le r\u00f4le du g\u00e9riatre dans la prise en charge de l'amylose cardiaque ?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1854\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"4\" role=\"region\" aria-labelledby=\"elementor-tab-title-1854\"><p>Un triple r\u00f4le : d\u00e9pister et diagnostiquer, orienter vers un centre de r\u00e9f\u00e9rence, et \u00e9valuer la fragilit\u00e9 pour optimiser la prise en charge.<\/p><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-2dcb18d elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"2dcb18d\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-df17308\" data-id=\"df17308\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-d96b649 elementor-widget elementor-widget-text-editor\" data-id=\"d96b649\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Chez le sujet \u00e2g\u00e9, l&rsquo;insuffisance cardiaque \u00e0 FEVG pr\u00e9serv\u00e9e est la forme la plus fr\u00e9quente d&rsquo;insuffisance cardiaque, et 15 \u00e0 20 % de ces patients ont potentiellement une amylose cardiaque sous-jacente. Le diagnostic doit \u00eatre \u00e9voqu\u00e9 devant des manifestations cardiaques (r\u00e9sistance au traitement habituel, microvoltage paradoxal), ost\u00e9o-articulaires (canal carpien, Dupuytren, canal lombaire \u00e9troit) ou neurosensorielles (neuropathie, macroglossie, dysautonomie). La fragilit\u00e9, tr\u00e8s fr\u00e9quente dans cette population (perte d&rsquo;autonomie 69 %, syndrome dysex\u00e9cutif 72 %, faiblesse musculaire 74 %), doit \u00eatre syst\u00e9matiquement \u00e9valu\u00e9e par le score SEGA puis par une \u00e9valuation g\u00e9riatrique approfondie multidimensionnelle. Le bilan diagnostique associe biomarqueurs, ECG et \u00e9chocardiographie en premi\u00e8re intention, compl\u00e9t\u00e9s si besoin par scintigraphie osseuse, IRM cardiaque et biopsie en milieu sp\u00e9cialis\u00e9. La prise en charge, men\u00e9e avec un centre de r\u00e9f\u00e9rence, repose sur un traitement sp\u00e9cifique (tafamidis pour l&rsquo;amylose TTR, chimioth\u00e9rapie pour l&rsquo;amylose AL). Le g\u00e9riatre a un triple r\u00f4le : d\u00e9pister et diagnostiquer, orienter vers un centre expert, et \u00e9valuer la fragilit\u00e9 pour optimiser la prise en charge.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<\/div>\n\t\t","protected":false},"excerpt":{"rendered":"<p>Pour le G\u00e9riatre D\u00e9pister, diagnostiquer et prendre en charge les amylose cardiaques Points cl\u00e9s pour les professionnels de sant\u00e9 15 \u00e0 20 % des patients \u00e2g\u00e9s hospitalis\u00e9s pour insuffisance cardiaque \u00e0 FEVG pr\u00e9serv\u00e9e ont potentiellement une amylose cardiaque sous-jacente. Trois manifestations doivent alerter : cardiaques (IC r\u00e9sistante, microvoltage paradoxal), ost\u00e9o-articulaires (canal carpien, Dupuytren, canal lombaire) [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_acf_changed":false,"footnotes":""},"categories":[],"tags":[],"class_list":["post-2827","page","type-page","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v25.5 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Amylose cardiaque \u2014 Ce que le g\u00e9riatre doit savoir - R\u00e9seau Amylose<\/title>\n<meta name=\"description\" content=\"D\u00e9pistage, diagnostic, fragilit\u00e9 et prise en charge de l&#039;amylose cardiaque chez le sujet \u00e2g\u00e9 \u2014 le triple r\u00f4le du g\u00e9riatre.\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/reseau-amylose.org\/jesuissoignant\/pour-le-geriatre\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Amylose cardiaque \u2014 Ce que le g\u00e9riatre doit savoir - 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