{"id":2777,"date":"2021-01-28T09:08:23","date_gmt":"2021-01-28T09:08:23","guid":{"rendered":"https:\/\/www.reseau-amylose.org\/jesuissoignant\/?page_id=2777"},"modified":"2025-11-14T16:22:25","modified_gmt":"2025-11-14T15:22:25","slug":"evaluation-du-pronostic-des-amyloses-les-scores","status":"publish","type":"page","link":"https:\/\/reseau-amylose.org\/jesuissoignant\/evaluation-du-pronostic-des-amyloses-les-scores\/","title":{"rendered":"Evaluation du pronostic des amyloses : les scores"},"content":{"rendered":"\t\t<div data-elementor-type=\"wp-page\" data-elementor-id=\"2777\" class=\"elementor elementor-2777\" data-elementor-post-type=\"page\">\n\t\t\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-be77b71 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"be77b71\" data-element_type=\"section\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-c8c7d97\" data-id=\"c8c7d97\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-d665792 elementor-widget elementor-widget-heading\" data-id=\"d665792\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h1 class=\"elementor-heading-title elementor-size-default\">Evaluation du pronostic des amyloses : les scores<\/h1>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-d7be9d2 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"d7be9d2\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-8bdebd1\" data-id=\"8bdebd1\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-91912e9 elementor-widget elementor-widget-heading\" data-id=\"91912e9\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Les scores pour l'\u00e9valuation du pronostic des amyloses AL en fonction des biomarqueurs<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-c58b0fb elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"c58b0fb\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-2c2d175\" data-id=\"2c2d175\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-f53a6b1 elementor-widget elementor-widget-text-editor\" data-id=\"f53a6b1\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<h6><span style=\"color: #000000\">Les scores pronostiques \u00e9voluent dans le temps. Ils permettent d\u2019estimer le pronostic du patient. Le score est d\u00e9fini par rapport aux valeurs basales avant la mise en route de la chimioth\u00e9rapie. Il est indicatif. Ils existent diff\u00e9rents types de marqueurs cardiaques (NTproBNP ou BNP, Troponine T (cTnT) ou Troponine I (cTNTi) ou Troponine T HS (HS-cTnT). Nous avons utilis\u00e9 la correspondance propos\u00e9e par Mutchar E et al (Blood 2019). sur les seuils. De m\u00eame pour les mesures de cha\u00eenes l\u00e9g\u00e8res o\u00f9 la plupart des articles ont \u00e9t\u00e9 publi\u00e9s en utilisant la technique binding site (freelite). La correspondance avec les autres tests comme la technique Siemens n\u2019est pas connue (Mutchar E, Letter to Blood, vol 133, number 7, feb 2019). La correspondance cTnT et HS-TnT a \u00e9t\u00e9 extrapol\u00e9e ainsi\u00a0: 0.025mg\/l \u00bb 40ng\/l\u00a0; 0.035mg\/l\u00a0 \u00bb 50\u00a0; 0.05mg\/l =65ng\/l\u00a0; 0.06mg\/lv \u00bb 75ng\/l\u00a0; pour la troponine I, il n\u2019y a pas d\u2019extrapolation propos\u00e9e.<\/span><\/h6><p><strong>\u00a0<\/strong><\/p><table width=\"640\"><tbody><tr><td width=\"102\"><p><strong>MAYO<\/strong><\/p><p><strong>2004<\/strong><\/p><\/td><td width=\"173\"><p><strong>cTnT\u22650.035 <\/strong><strong>m<\/strong><strong>g\/l<\/strong><\/p><p><strong>ou<\/strong><\/p><p><strong>HS-cTnT\u00a0 \u226550 ng\/l<\/strong><\/p><\/td><td width=\"192\"><p><strong>NTproBNP \u2265332 pg\/ml<\/strong><\/p><p><strong>BNP &gt; 81 ng\/L<\/strong><\/p><\/td><td width=\"173\"><p><strong>HR pour le d\u00e9c\u00e8s<\/strong><\/p><p><strong>(95%CI)<\/strong><\/p><\/td><\/tr><tr><td width=\"102\"><p><strong>I<\/strong><\/p><\/td><td width=\"173\"><p><strong>0<\/strong><\/p><\/td><td width=\"192\"><p><strong>0<\/strong><\/p><\/td><td width=\"173\"><p><strong>R\u00e9f\u00e9rence<\/strong><\/p><\/td><\/tr><tr><td width=\"102\"><p><strong>II<\/strong><\/p><\/td><td colspan=\"2\" width=\"365\"><p><strong>1 des 2<\/strong><\/p><\/td><td width=\"173\"><p><strong>2.5 (1.9-3.5)<\/strong><\/p><\/td><\/tr><tr><td width=\"102\"><p><strong>III<\/strong><\/p><\/td><td width=\"173\"><p><strong>1<\/strong><\/p><\/td><td width=\"192\"><p><strong>1<\/strong><\/p><\/td><td width=\"173\"><p><strong>6.7 (5.0-9.1)<\/strong><\/p><\/td><\/tr><\/tbody><\/table><p><em>R\u00e9f\u00e9rence : <\/em><em>Dispenzieri A, Gertz MA, Kyle RA, J Clin Oncol. 2004 Sep 15;22(18):3751-7.<\/em><\/p><table width=\"640\"><tbody><tr><td width=\"102\"><p><strong>MAYO<\/strong><\/p><p><strong>2012<\/strong><\/p><\/td><td width=\"132\"><p><strong>cTNT\u22650.025 ng\/ml<\/strong><\/p><p><strong>ou<\/strong><\/p><p><strong>HS-cTnT \u2265 40 ng\/l<\/strong><\/p><\/td><td width=\"151\"><p><strong>NTproBNP \u22651800pg\/ml<\/strong><\/p><\/td><td width=\"123\"><p><strong>dFLC \u226518 mg\/dl<\/strong><\/p><p><strong>ou<\/strong><\/p><p><strong>dFlc \u2265 180mg\/l<\/strong><\/p><\/td><td width=\"132\"><p><strong>HR pour le d\u00e9c\u00e8s<\/strong><\/p><p><strong>(95%CI)<\/strong><\/p><\/td><\/tr><tr><td width=\"102\"><p><strong>I<\/strong><\/p><\/td><td width=\"132\"><p><strong>0<\/strong><\/p><\/td><td width=\"151\"><p><strong>0<\/strong><\/p><\/td><td width=\"123\"><p><strong>0<\/strong><\/p><\/td><td width=\"132\"><p><strong>R\u00e9f\u00e9rence<\/strong><\/p><\/td><\/tr><tr><td width=\"102\"><p><strong>II<\/strong><\/p><\/td><td colspan=\"3\" width=\"406\"><p><strong>1 augment\u00e9<\/strong><\/p><\/td><td width=\"132\"><p><strong>1.7 (1.2 -2.3)<\/strong><\/p><\/td><\/tr><tr><td width=\"102\"><p><strong>III<\/strong><\/p><\/td><td colspan=\"3\" width=\"406\"><p><strong>2 augment\u00e9<\/strong><\/p><\/td><td width=\"132\"><p><strong>4.1 (3.1 \u2013 5.5)<\/strong><\/p><\/td><\/tr><tr><td width=\"102\"><p><strong>IV<\/strong><\/p><\/td><td width=\"132\"><p><strong>1<\/strong><\/p><\/td><td width=\"151\"><p><strong>1<\/strong><\/p><\/td><td width=\"123\"><p><strong>1<\/strong><\/p><\/td><td width=\"132\"><p><strong>6.3 (4.8 \u2013 8.3)<\/strong><\/p><\/td><\/tr><\/tbody><\/table><p><em>R\u00e9f\u00e9rence : Kumar <\/em><em>S, Disperenzieri, \u00a0et al J Clin Oncol 2012 Mar 20\u00a0; 30(9)\u00a0:989-95 <\/em><\/p><table width=\"640\"><tbody><tr><td width=\"102\"><p><strong>EUROPEAN<\/strong><\/p><p><strong>\u00a0<\/strong><strong>2015<\/strong><\/p><\/td><td width=\"170\"><p><strong>cTNT \u22650.035 ng\/ml<\/strong><\/p><p><strong>TNT-hs \u2265 50 ng\/l<\/strong><\/p><\/td><td width=\"198\"><p><strong>NTproBNP \u2265332 pg\/ml<\/strong><\/p><p><strong>BNP &gt; 81 ng\/L<\/strong><\/p><\/td><td width=\"170\"><p><strong>HR pour le d\u00e9c\u00e8s<\/strong><\/p><p><strong>(95%CI)<\/strong><\/p><\/td><\/tr><tr><td width=\"102\"><p><strong>I<\/strong><\/p><\/td><td width=\"170\"><p><strong>0<\/strong><\/p><\/td><td width=\"198\"><p><strong>0<\/strong><\/p><\/td><td width=\"170\"><p><strong>R\u00e9f\u00e9rence<\/strong><\/p><\/td><\/tr><tr><td width=\"102\"><p><strong>II<\/strong><\/p><\/td><td colspan=\"2\" width=\"369\"><p><strong>1 des 2<\/strong><\/p><\/td><td width=\"170\"><p><strong>2.6 (1.9-3.5)<\/strong><\/p><\/td><\/tr><tr><td width=\"102\"><p><strong>III-a<\/strong><\/p><\/td><td width=\"170\"><p><strong>1<\/strong><\/p><\/td><td width=\"198\"><p><strong>1<\/strong><\/p><\/td><td width=\"170\"><p><strong>4.9 (3.6-6.8)<\/strong><\/p><\/td><\/tr><tr><td width=\"102\"><p><strong>III-b<\/strong><\/p><\/td><td width=\"170\"><p><strong>1<\/strong><\/p><\/td><td width=\"198\"><p><strong>NTproBNP &gt;8500 ng\/l<\/strong><\/p><p><strong>BNP &gt;700ng \/L<\/strong><\/p><\/td><td width=\"170\"><p><strong>11.1 (8.1-15.4)<\/strong><\/p><\/td><\/tr><\/tbody><\/table><p><em>R\u00e9f\u00e9rence\u00a0:<\/em> <em>Palladini G<\/em><em>, Sachchithanantham S, Milani P, Blood. 2015 Jul 30;126(5):612-5.<\/em><\/p><h5><strong>Lien pour pubmed des articles r\u00e9f\u00e9renc\u00e9s\u00a0: Scores Amylose AL<\/strong><\/h5><p><a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/30545829\/\"><em>Staging<\/em><em> systems use for risk stratification of systemic amyloidosis in the era of high-sensitivity troponin T assay. <\/em><\/a><\/p><p><em>Muchtar E<\/em><em>, Kumar SK, Gertz MA, Grogan M, AbouEzzeddine OF, Jaffe AS, Dispenzieri A. Blood. <\/em><em>2019 Feb 14;133(7):763-766. doi: 10.1182\/blood-2018-10-875252. Epub 2018 Dec 13. PMID: 30545829 <\/em><\/p><p><em>\u00a0<\/em><\/p><p><em>MAYO 2004\u00a0:<\/em> <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/15365071\/\"><em>Serum<\/em><em> cardiac troponins and N-terminal pro-brain natriuretic peptide: a staging system for primary systemic amyloidosis. <\/em><\/a><em>Dispenzieri A, Gertz MA, Kyle RA, Lacy MQ, Burritt MF, Therneau TM, Greipp PR, Witzig TE, Lust JA, Rajkumar SV, Fonseca R, Zeldenrust SR, McGregor CG, Jaffe AS. <\/em><em>J Clin Oncol. 2004 Sep 15;22(18):3751-7. doi: 10.1200\/JCO.2004.03.029. PMID: 15365071 <\/em><\/p><p><em>EUROPEAN 2015\u00a0: <\/em><a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/25987656\/\"><em>A European collaborative study of cyclophosphamide, bortezomib, and dexamethasone in upfront treatment of systemic AL amyloidosis. <\/em><\/a><em>Palladini G<\/em><em>, Sachchithanantham S, Milani P, Gillmore J, Foli A, Lachmann H, Basset M, Hawkins P, Merlini G, Wechalekar AD. Blood. 2015 Jul 30;126(5):612-5. doi: 10.1182\/blood-2015-01-620302. Epub 2015 May 18. PMID: 25987656 <\/em><\/p><p><em>\u00a0<\/em><\/p><p><em>MAYO 2012\u00a0: <\/em><a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/22331953\/\"><em>Revised prognostic staging system for light chain amyloidosis incorporating cardiac biomarkers and serum free light chain measurements. <\/em><\/a><em>Kumar S<\/em><em>, Dispenzieri A, Lacy MQ, Hayman SR, Buadi FK, Colby C, Laumann K, Zeldenrust SR, Leung N, Dingli D, Greipp PR, Lust JA, Russell SJ, Kyle RA, Rajkumar SV, Gertz MA. <\/em><em>J Clin Oncol. 2012 Mar 20;30(9):989-95. doi: 10.1200\/JCO.2011.38.5724. Epub 2012 Feb 13. PMID: 22331953 <\/em><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-027b168 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"027b168\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-16 elementor-top-column elementor-element elementor-element-24d15ae\" data-id=\"24d15ae\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap\">\n\t\t\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-66 elementor-top-column elementor-element elementor-element-1b17112\" data-id=\"1b17112\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-7bb2dab elementor-widget elementor-widget-image\" data-id=\"7bb2dab\" data-element_type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<a href=\"http:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2024\/04\/PLAQUETTE-Pronostic-AL-sans-mediane-de-survie-1.pdf\" target=\"_blank\">\n\t\t\t\t\t\t\t<img fetchpriority=\"high\" decoding=\"async\" width=\"1024\" height=\"769\" src=\"https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2024\/04\/evaluation-Pronostic-amyloses-AL-scores-copie.jpg\" class=\"attachment-large size-large wp-image-6459\" alt=\"\" \/>\t\t\t\t\t\t\t\t<\/a>\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-16 elementor-top-column elementor-element elementor-element-5a46471\" data-id=\"5a46471\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap\">\n\t\t\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-d55848d elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"d55848d\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-dbcc53e\" data-id=\"dbcc53e\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-04cf8a5 elementor-cta--skin-cover elementor-animated-content elementor-bg-transform elementor-bg-transform-zoom-in elementor-widget elementor-widget-call-to-action\" data-id=\"04cf8a5\" data-element_type=\"widget\" data-widget_type=\"call-to-action.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<a class=\"elementor-cta\" href=\"http:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2024\/04\/Scores-Pronostiques-des-Amyloses-AL-pour-site-web-1.pdf\" target=\"_blank\">\n\t\t\t\t\t<div class=\"elementor-cta__bg-wrapper\">\n\t\t\t\t<div class=\"elementor-cta__bg elementor-bg\" style=\"background-image: url(https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2021\/01\/Capture-de\u0301cran-2021-01-28-a\u0300-10.13.21-1024x649.png);\" role=\"img\" aria-label=\"Capture d\u2019e\u0301cran 2021-01-28 a\u0300 10.13.21\"><\/div>\n\t\t\t\t<div class=\"elementor-cta__bg-overlay\"><\/div>\n\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-cta__content\">\n\t\t\t\t\n\t\t\t\t\t\t\t\t\t<h2 class=\"elementor-cta__title elementor-cta__content-item elementor-content-item elementor-animated-item--grow\">\n\t\t\t\t\t\tScores Pronostiques des Amyloses AL\t\t\t\t\t<\/h2>\n\t\t\t\t\n\t\t\t\t\n\t\t\t\t\t\t\t\t\t<div class=\"elementor-cta__button-wrapper elementor-cta__content-item elementor-content-item elementor-animated-item--grow\">\n\t\t\t\t\t<span class=\"elementor-cta__button elementor-button elementor-size-\">\n\t\t\t\t\t\tT\u00c9L\u00c9CHARGER LE DOCUMENT\t\t\t\t\t<\/span>\n\t\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\t\t<\/a>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-f1cd35f\" data-id=\"f1cd35f\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-7c34736 elementor-cta--skin-cover elementor-animated-content elementor-bg-transform elementor-bg-transform-zoom-in elementor-widget elementor-widget-call-to-action\" data-id=\"7c34736\" data-element_type=\"widget\" data-widget_type=\"call-to-action.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<a class=\"elementor-cta\" href=\"http:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2024\/04\/Scores-Pronostiques-des-Amyloses-TTR-pour-site-web.pdf\" target=\"_blank\">\n\t\t\t\t\t<div class=\"elementor-cta__bg-wrapper\">\n\t\t\t\t<div class=\"elementor-cta__bg elementor-bg\" style=\"background-image: url(https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2021\/01\/Capture-de\u0301cran-2021-01-28-a\u0300-10.19.39-1024x747.png);\" role=\"img\" aria-label=\"Capture d\u2019e\u0301cran 2021-01-28 a\u0300 10.19.39\"><\/div>\n\t\t\t\t<div class=\"elementor-cta__bg-overlay\"><\/div>\n\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-cta__content\">\n\t\t\t\t\n\t\t\t\t\t\t\t\t\t<h2 class=\"elementor-cta__title elementor-cta__content-item elementor-content-item elementor-animated-item--grow\">\n\t\t\t\t\t\tScores Pronostiques des Amyloses TTR\t\t\t\t\t<\/h2>\n\t\t\t\t\n\t\t\t\t\n\t\t\t\t\t\t\t\t\t<div class=\"elementor-cta__button-wrapper elementor-cta__content-item elementor-content-item elementor-animated-item--grow\">\n\t\t\t\t\t<span class=\"elementor-cta__button elementor-button elementor-size-\">\n\t\t\t\t\t\tT\u00c9L\u00c9CHARGER LE DOCUMENT\t\t\t\t\t<\/span>\n\t\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\t\t<\/a>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-633b83d elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"633b83d\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-7eddace\" data-id=\"7eddace\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-04450e3 elementor-widget elementor-widget-text-editor\" data-id=\"04450e3\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<h4><span style=\"color: #4db8f0\"><strong>Scores pronostiques <\/strong><strong>des amyloses \u00e0 transthyr\u00e9tine s\u00e9niles et h\u00e9r\u00e9ditaires (ATTRwt et ATTRv)<\/strong><\/span><\/h4><h6><span style=\"color: #000000\">Les scores pronostiques \u00e9voluent dans le temps. Ils permettent d\u2019estimer le pronostic du patient. Ils sont indicatifs.<\/span><\/h6><h6><span style=\"color: #000000\">Ils existent diff\u00e9rents types de marqueurs cardiaques (NTproBNP ou BNP, Troponine T (cTnT) ou Troponine I (cTNTi) ou Troponine T HS (HS-cTnT).<\/span><\/h6><h6><span style=\"color: #000000\">Nous avons utilis\u00e9 la correspondance propos\u00e9e par Dispenzieri A. sur les seuils. De m\u00eame pour les mesures de cha\u00eenes l\u00e9g\u00e8res o\u00f9 la plupart des articles ont \u00e9t\u00e9 publi\u00e9s en utilisant la technique binding site (freelite). La correspondance avec les autres tests comme la technique Siemens n\u2019est pas connue (Mutchar E, Letter to blood, vol 133, number 7, feb 2019).<\/span><\/h6><p><strong>\u00a0<\/strong><\/p><table width=\"640\"><tbody><tr><td width=\"102\"><p><strong>MAYO<\/strong><\/p><p><strong>TTR<\/strong><\/p><\/td><td width=\"189\"><p><strong>cTnT &gt;0.05<\/strong><\/p><p><strong>HS-cTnT <\/strong><strong>\u226565 ng\/l<\/strong><\/p><\/td><td width=\"176\"><p><strong>NT-proBNP &gt; 3000<\/strong><\/p><\/td><td width=\"173\"><p><strong>HR pour le d\u00e9c\u00e8s<\/strong><\/p><p><strong>(95%CI)<\/strong><\/p><\/td><\/tr><tr><td width=\"102\"><p><strong>I<\/strong><\/p><\/td><td width=\"189\"><p><strong>0<\/strong><\/p><\/td><td width=\"176\"><p><strong>0<\/strong><\/p><\/td><td width=\"173\"><p><strong>R\u00e9f\u00e9rence<\/strong><\/p><\/td><\/tr><tr><td width=\"102\"><p><strong>II<\/strong><\/p><\/td><td colspan=\"2\" width=\"365\"><p><strong>1 des 2<\/strong><\/p><\/td><td width=\"173\"><p><strong>1.4 (0.8 \u2013 2.6)<\/strong><\/p><\/td><\/tr><tr><td width=\"102\"><p><strong>III<\/strong><\/p><\/td><td width=\"189\"><p><strong>1<\/strong><\/p><\/td><td width=\"176\"><p><strong>1<\/strong><\/p><\/td><td width=\"173\"><p><strong>3.6 (2.0 \u2013 6.4)<\/strong><\/p><\/td><\/tr><\/tbody><\/table><p><em>R\u00e9f\u00e9rence : Grogan M, Scott CG, Kyle RA et al, JACC 2016; 68 (10) :1014-1020<\/em><\/p><p><strong>\u00a0<\/strong><\/p><table width=\"640\"><tbody><tr><td width=\"102\"><p><strong>NAC<\/strong><\/p><\/td><td width=\"189\"><p><strong>eGFR &lt;45mL\/min\/1.73m\u00b2<\/strong><\/p><\/td><td width=\"176\"><p><strong>NT-proBNP &gt; 3000<\/strong><\/p><\/td><td width=\"173\"><p><strong>HR pour le d\u00e9c\u00e8s<\/strong><\/p><p><strong>(95%CI)<\/strong><\/p><\/td><\/tr><tr><td width=\"102\"><p><strong>I<\/strong><\/p><\/td><td width=\"189\"><p><strong>0<\/strong><\/p><\/td><td width=\"176\"><p><strong>0<\/strong><\/p><\/td><td width=\"173\"><p><strong>R\u00e9f\u00e9rence<\/strong><\/p><\/td><\/tr><tr><td width=\"102\"><p><strong>II<\/strong><\/p><\/td><td colspan=\"2\" width=\"365\"><p><strong>1 des 2<\/strong><\/p><\/td><td width=\"173\"><p><strong>2.1 (1.5-2.8)<\/strong><\/p><\/td><\/tr><tr><td width=\"102\"><p><strong>III<\/strong><\/p><\/td><td width=\"189\"><p><strong>1<\/strong><\/p><\/td><td width=\"176\"><p><strong>1<\/strong><\/p><\/td><td width=\"173\"><p><strong>3.8 (2.7-5.3)<\/strong><\/p><\/td><\/tr><\/tbody><\/table><p><em>R\u00e9f\u00e9rence : Gillmore JD, Damy T, Fontana M et al, Eur Heart J 2018 Aug 7; 39:2799-2806<\/em><\/p><p><em>\u00a0<\/em><\/p><p><em>\u00a0<\/em><\/p><h5><strong>Lien pour pubmed des articles r\u00e9f\u00e9renc\u00e9s\u00a0: Scores Amyloses TTR<\/strong><\/h5><p><a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/30545829\/\"><em>Staging<\/em><em> systems use for risk stratification of systemic amyloidosis in the era of high-sensitivity troponin T assay. <\/em><\/a><\/p><p><em>Muchtar E<\/em><em>, Kumar SK, Gertz MA, Grogan M, AbouEzzeddine OF, Jaffe AS, Dispenzieri A. Blood. <\/em><em>2019 Feb 14;133(7):763-766. doi: 10.1182\/blood-2018-10-875252. Epub 2018 Dec 13. PMID: 30545829 <\/em><\/p><p><em>Haut du formulaire<\/em><\/p><p><em>Bas du formulaire<\/em><\/p><p><a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/27585505\/\"><em>Natural History of Wild-Type Transthyretin\u00a0Cardiac Amyloidosis and\u00a0Risk Stratification Using a Novel\u00a0Staging System. <\/em><\/a><\/p><p><em>Grogan M<\/em><em>, Scott CG, Kyle RA, Zeldenrust SR, Gertz MA, Lin G, Klarich KW, Miller WL, Maleszewski JJ, Dispenzieri A. J Am Coll Cardiol. 2016 Sep 6;68(10):1014-20. doi: 10.1016\/j.jacc.2016.06.033.<\/em><\/p><p><a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/29048471\/\"><em>A new staging system for cardiac transthyretin amyloidosis. <\/em><\/a><\/p><p><em>Gillmore JD<\/em><em>, Damy T, Fontana M, Hutchinson M, Lachmann HJ, Martinez-Naharro A, Quarta CC, Rezk T, Whelan CJ, Gonzalez-Lopez E, Lane T, Gilbertson JA, Rowczenio D, Petrie A, Hawkins PN. <\/em><em>Eur Heart J. 2018 Aug 7;39(30):2799-2806. doi: 10.1093\/eurheartj\/ehx589.<\/em><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-befc63d elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"befc63d\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-960ff8c\" data-id=\"960ff8c\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-9139da9 elementor-widget elementor-widget-text-editor\" data-id=\"9139da9\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Plus r\u00e9cemment, on a d\u00e9velopp\u00e9 un nouveau score sur une population de patients atteints d\u2019<b>amylose<\/b> <b>h\u00e9r\u00e9ditaire<\/b><b> \u00e0 <\/b><b>transthyr\u00e9tine<\/b><b> (<\/b><b>ATTRv<\/b><b>) <\/b><b>d\u00e9j\u00e0<\/b> <b>trait\u00e9s<\/b><b> par <\/b><b>th\u00e9rapies<\/b> <b>sp\u00e9cifiques<\/b><b> (<\/b><b>dont<\/b><b> le <\/b><b>Tafamidis<\/b><b>)<\/b>, reposant sur trois crit\u00e8res<\/p><ul><li>Strain Globale Longitudinale (GLS) \u2265 -11 %<\/li><li>NT-proBNP \u2265 2000 ng\/L<\/li><li>eGFR \u2264 65 mL\/min<\/li><\/ul><p>Selon la classification, on peut distinguer <b>trois stades pronostiques <\/b>avec des survies \u00e0 5 ans tr\u00e8s diff\u00e9rentes :<\/p><ul><li>Stade I : aucun crit\u00e8re pr\u00e9sent (survie \u2248 98,5 %)<\/li><li>Stade II : un crit\u00e8re pr\u00e9sent (survie \u2248 75,1 %)<\/li><li>Stade III : GLS \u2265 -11 % + au moins 1 autre crit\u00e8re (survie \u2248 29,4 %)<\/li><\/ul><p><b>R\u00e9f\u00e9rence<\/b> : Neculae G, Zaroui A, Adam R, Kharoubi M, Funalot B, Coriu D, Jurcut R, Damy T. <i>A <\/i><i>new<\/i> <i>staging<\/i> <i>system<\/i><i> for <\/i><i>hereditary<\/i> <i>transthyretin<\/i> <i>amyloidosis<\/i><i> in <\/i><i>the<\/i><i> era of specific <\/i><i>amyloidosis<\/i> <i>therapies<\/i>. ESC Heart Failure. 2025. doi:10.1002\/ehf2.15414. PMID: 40903446.<\/p><table width=\"902\"><tbody><tr><td width=\"117\"><p><b>Stade<\/b><\/p><\/td><td width=\"155\"><p><b>GLS \u2265 -11 %<\/b><\/p><\/td><td width=\"82\">\u00a0<\/td><td width=\"155\"><p><b>NT-proBNP \u2265 2000 ng\/L<\/b><\/p><\/td><td width=\"82\">\u00a0<\/td><td width=\"155\"><p><b>eGFR<\/b><b> \u2264 65 <\/b><b>mL<\/b><b>\/min<\/b><\/p><\/td><td width=\"155\"><p><b>HR pour le d\u00e9c\u00e8s<\/b><\/p><p><b>(95%CI)<\/b><\/p><\/td><\/tr><tr><td width=\"117\"><p><b>I<\/b><\/p><\/td><td width=\"155\"><p><b>0<\/b><\/p><\/td><td width=\"82\"><p><b>et<\/b><\/p><\/td><td width=\"155\"><p><b>0<\/b><\/p><\/td><td width=\"82\"><p><b>et<\/b><\/p><\/td><td width=\"155\"><p><b>0<\/b><\/p><\/td><td width=\"155\"><p><b>R\u00e9f\u00e9rence<\/b><\/p><\/td><\/tr><tr><td rowspan=\"2\" width=\"117\"><p><b>II<\/b><\/p><\/td><td width=\"155\"><p><b>1<\/b><\/p><\/td><td width=\"82\"><p><b>ou<\/b><\/p><\/td><td width=\"155\"><p><b>1<\/b><\/p><\/td><td width=\"82\"><p><b>ou<\/b><\/p><\/td><td width=\"155\"><p><b>1<\/b><\/p><\/td><td rowspan=\"2\" width=\"155\"><p><b>13.47 (1.79-101.67)<\/b><\/p><\/td><\/tr><tr><td width=\"155\"><p><b>0<\/b><\/p><\/td><td width=\"82\"><p><b>et<\/b><\/p><\/td><td width=\"155\"><p><b>1<\/b><\/p><\/td><td width=\"82\"><p><b>et<\/b><\/p><\/td><td width=\"155\"><p><b>1<\/b><\/p><\/td><\/tr><tr><td width=\"117\"><p><b>III<\/b><\/p><\/td><td width=\"155\"><p><b>1<\/b><\/p><\/td><td width=\"82\"><p><b>et<\/b><\/p><\/td><td colspan=\"3\" width=\"392\"><p><b>1 des 2 <\/b><b>ou<\/b><b> les 2<\/b><\/p><\/td><td width=\"155\"><p><b>54.3 (7.45-396.04)<\/b><\/p><\/td><\/tr><\/tbody><\/table><p><em>Neculae G, Zaroui A, Adam R, Kharoubi M, Funalot B, Coriu D, Jurcut R, Damy T. ESC Heart Failure. 2025 &#8211; <a href=\"https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2025\/11\/Amyloidosis-PROGNOSIS-New-Prognostic-Staging-Neculae-ESC-HF-2025.pdf\" target=\"_blank\" rel=\"noopener\">lien vers l&rsquo;article<\/a><\/em><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-bd9f94a elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"bd9f94a\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-f79db5c\" data-id=\"f79db5c\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-8942d6f elementor-widget elementor-widget-image\" data-id=\"8942d6f\" data-element_type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img decoding=\"async\" width=\"1024\" height=\"456\" src=\"https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2025\/11\/score-pronostic-ATTR-reseau-amylose-1024x456.jpg\" class=\"attachment-large size-large wp-image-7329\" alt=\"score-pronostic-ATTR-re\u0301seau-amylose\" srcset=\"https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2025\/11\/score-pronostic-ATTR-reseau-amylose-1024x456.jpg 1024w, https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2025\/11\/score-pronostic-ATTR-reseau-amylose-300x133.jpg 300w, https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2025\/11\/score-pronostic-ATTR-reseau-amylose-768x342.jpg 768w, https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2025\/11\/score-pronostic-ATTR-reseau-amylose-1536x683.jpg 1536w, https:\/\/reseau-amylose.org\/jesuissoignant\/wp-content\/uploads\/sites\/5\/2025\/11\/score-pronostic-ATTR-reseau-amylose-2048x911.jpg 2048w\" sizes=\"(max-width: 1024px) 100vw, 1024px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<\/div>\n\t\t","protected":false},"excerpt":{"rendered":"<p>Evaluation du pronostic des amyloses : les scores Les scores pour l&rsquo;\u00e9valuation du pronostic des amyloses AL en fonction des biomarqueurs Les scores pronostiques \u00e9voluent dans le temps. Ils permettent d\u2019estimer le pronostic du patient. Le score est d\u00e9fini par rapport aux valeurs basales avant la mise en route de la chimioth\u00e9rapie. Il est indicatif. [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_monsterinsights_skip_tracking":false,"_monsterinsights_sitenote_active":false,"_monsterinsights_sitenote_note":"","_monsterinsights_sitenote_category":0,"footnotes":""},"categories":[],"tags":[],"class_list":["post-2777","page","type-page","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v25.5 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Evaluation du pronostic des amyloses : les scores - R\u00e9seau Amylose<\/title>\n<meta name=\"description\" content=\"Amylose AL, amylose TTR h\u00e9r\u00e9ditaire ou sauvage - Evaluation du pronostic des amyloses : les scores - consultez les scores de l&#039;amylose\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"http:\/\/reseau-amylose.org\/jesuissoignant\/evaluation-du-pronostic-des-amyloses-les-scores\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Evaluation du pronostic des amyloses : les scores - 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