{"id":3548,"date":"2021-04-14T12:06:25","date_gmt":"2021-04-14T12:06:25","guid":{"rendered":"https:\/\/www.reseau-amylose.org\/jesuissoignant\/?page_id=3548"},"modified":"2026-08-10T16:41:36","modified_gmt":"2026-08-10T14:41:36","slug":"examens-complementaires-electrocardiogramme-le-bilan-biologique-de-l-amylose","status":"publish","type":"page","link":"http:\/\/reseau-amylose.org\/jesuissoignant\/examens-complementaires-electrocardiogramme-le-bilan-biologique-de-l-amylose\/","title":{"rendered":"Le bilan biologique de l&rsquo;amylose"},"content":{"rendered":"\t\t<div data-elementor-type=\"wp-page\" data-elementor-id=\"3548\" class=\"elementor elementor-3548\" data-elementor-post-type=\"page\">\n\t\t\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-b187054 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"b187054\" data-element_type=\"section\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-bf47f8c\" data-id=\"bf47f8c\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-78052fb elementor-widget elementor-widget-heading\" data-id=\"78052fb\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h1 class=\"elementor-heading-title elementor-size-default\">Le bilan biologique de l'amylose<\/h1>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-50978dd6 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"50978dd6\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-79374f4\" data-id=\"79374f4\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-2dc8a176 elementor-widget elementor-widget-text-editor\" data-id=\"2dc8a176\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Les examens compl\u00e9mentaires cardiaques permettent de <strong>suspecter<\/strong> l&rsquo;amylose. Seul le <strong>diagnostic anatomopathologique<\/strong> permet de l&rsquo;affirmer. L&rsquo;\u00e9chocardiographie, l&rsquo;IRM et la scintigraphie sont compl\u00e9mentaires dans l&rsquo;approche diagnostique, toutefois ces examens ne permettent pas de distinguer avec certitude les diff\u00e9rentes formes d&rsquo;amylose. Le bilan biologique de l&rsquo;amylose est important et participe au typage de l&rsquo;amylose.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-88eb5e6 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"88eb5e6\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-151cb2b\" data-id=\"151cb2b\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-7fd030e elementor-widget elementor-widget-heading\" data-id=\"7fd030e\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Points cl\u00e9s pour les professionnels de sant\u00e9<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-3de5eba elementor-widget elementor-widget-text-editor\" data-id=\"3de5eba\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<ul><li>Les peptides natriur\u00e9tiques et la troponine sont fr\u00e9quemment \u00e9lev\u00e9s dans la cardiopathie amylo\u00efde, en l&rsquo;absence de coronaropathie.<\/li><li>Un score de gravit\u00e9 bas\u00e9 sur ces biomarqueurs (Mayo Clinic) guide le protocole de chimioth\u00e9rapie et le suivi dans les amyloses AL.<\/li><li>Le diagnostic d&rsquo;AL n\u00e9cessite syst\u00e9matiquement : \u00e9lectrophor\u00e8se des protides, immunofixation, cha\u00eenes l\u00e9g\u00e8res libres s\u00e9riques, prot\u00e9inurie de Bence Jones.<\/li><li>Un test g\u00e9n\u00e9tique du g\u00e8ne de la transthyr\u00e9tine doit \u00eatre r\u00e9alis\u00e9 chez tous les patients porteurs d&rsquo;une amylose ATTR.<\/li><\/ul>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-df22f46 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"df22f46\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-1256a9fb\" data-id=\"1256a9fb\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-3b69acb elementor-widget elementor-widget-heading\" data-id=\"3b69acb\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Biomarqueurs cardiaques dans le bilan biologique de l'amylose<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-22ad9865 elementor-widget elementor-widget-text-editor\" data-id=\"22ad9865\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Les peptides natriur\u00e9tiques sont fr\u00e9quemment augment\u00e9s dans les formes s\u00e9v\u00e8res de cardiopathie amylo\u00efde. La troponine I et T sont fr\u00e9quemment augment\u00e9es dans la cardiopathie amylo\u00efde en l&rsquo;absence de coronaropathie. L&rsquo;\u00e9l\u00e9vation de ces marqueurs t\u00e9moigne de la souffrance des cardiomyocytes du fait de l&rsquo;infiltration myocardique.<\/p><p>L&rsquo;\u00e9l\u00e9vation de la troponine ainsi que des pseudo-ondes Q \u00e0 l&rsquo;ECG conduit fr\u00e9quemment \u00e0 la r\u00e9alisation d&rsquo;une coronarographie chez ces patients. Une coronarographie normale dans ce contexte doit faire r\u00e9aliser une \u00e9chocardiographie \u00e0 la recherche d&rsquo;un \u00e9paississement myocardique.<\/p><p>L&rsquo;\u00e9l\u00e9vation des marqueurs a permis d&rsquo;\u00e9tablir un score de gravit\u00e9 dans les amyloses AL (Mayo Clinic), qui d\u00e9finit le protocole de chimioth\u00e9rapie et permet le suivi des patients. La diminution des marqueurs traduit la r\u00e9ponse \u00e0 la chimioth\u00e9rapie et est un facteur de bon pronostic. Des scores utilisant soit le <a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/27585505\/\" target=\"_blank\" rel=\"noopener\">NTproBNP et la troponine<\/a> ou soit le\u00a0<a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/29048471\/\" target=\"_blank\" rel=\"noopener\">NTproBNP et la fonction r\u00e9nale<\/a>\u00a0permettent \u00e9galement de pr\u00e9dire le pronostic dans les amyloses \u00e0 transthyr\u00e9tine.<\/p><p>\u00a0<\/p><p><em><a href=\"https:\/\/pubmed.ncbi.nlm.nih.gov\/27647161\/\" target=\"_blank\" rel=\"noopener\">Damy T et al, Amyloid 2016<\/a> <\/em><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-e73b7fc elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"e73b7fc\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-6d11d33\" data-id=\"6d11d33\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-7602a95 elementor-widget elementor-widget-text-editor\" data-id=\"7602a95\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<h4><strong>Biomarqueurs cardiaques <\/strong><\/h4><h4>Pr Damien Logeart<\/h4>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-e698b6d\" data-id=\"e698b6d\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-23f25f4 elementor-widget elementor-widget-video\" data-id=\"23f25f4\" data-element_type=\"widget\" data-settings=\"{&quot;youtube_url&quot;:&quot;https:\\\/\\\/www.youtube.com\\\/watch?v=LGerhRcXY5w&quot;,&quot;video_type&quot;:&quot;youtube&quot;,&quot;controls&quot;:&quot;yes&quot;}\" data-widget_type=\"video.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-wrapper elementor-open-inline\">\n\t\t\t<div class=\"elementor-video\"><\/div>\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-5fb795e7 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"5fb795e7\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-4bfdf501\" data-id=\"4bfdf501\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-477a3cf elementor-widget elementor-widget-heading\" data-id=\"477a3cf\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Rechercher une gammapathie : le bilan biologique de l'amylose<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-64bbf963 elementor-widget elementor-widget-text-editor\" data-id=\"64bbf963\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Le diagnostic des amyloses AL n\u00e9cessite la r\u00e9alisation d&rsquo;une \u00e9lectrophor\u00e8se des protides, d&rsquo;une immunofixation, du dosage des cha\u00eenes l\u00e9g\u00e8res libres s\u00e9riques et de la recherche d&rsquo;une prot\u00e9inurie de Bence Jones. Le bilan biologique identifie le pic monoclonal et permet de quantifier les cha\u00eenes kappa et lambda. L&rsquo;analyse du g\u00e8ne de la transthyr\u00e9tine par s\u00e9quen\u00e7age est n\u00e9cessaire pour \u00e9tablir le diagnostic d&rsquo;amylose h\u00e9r\u00e9ditaire \u00e0 transthyr\u00e9tine.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-333e744a elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"333e744a\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-83e9fb6\" data-id=\"83e9fb6\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-73e6b3a elementor-widget elementor-widget-heading\" data-id=\"73e6b3a\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Comment rechercher une gammapathie quand on suspecte une amylose<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-c795778 elementor-widget elementor-widget-heading\" data-id=\"c795778\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">Dr Val\u00e9rie MOLINIER-FRENKEL<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-2c451062 elementor-widget elementor-widget-video\" data-id=\"2c451062\" data-element_type=\"widget\" data-settings=\"{&quot;youtube_url&quot;:&quot;https:\\\/\\\/www.youtube.com\\\/watch?v=rosyfF4oddY&amp;ab_channel=R%C3%A9seauAmylose&quot;,&quot;video_type&quot;:&quot;youtube&quot;,&quot;controls&quot;:&quot;yes&quot;}\" data-widget_type=\"video.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-wrapper elementor-open-inline\">\n\t\t\t<div class=\"elementor-video\"><\/div>\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-51c0c118\" data-id=\"51c0c118\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-a9e9b2f elementor-widget elementor-widget-heading\" data-id=\"a9e9b2f\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Comment faire le diagnostic pr\u00e9coce des amyloses AL ?<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-156a3e5 elementor-widget elementor-widget-heading\" data-id=\"156a3e5\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">Dr Olivier DECAUX<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-1963fe31 elementor-widget elementor-widget-video\" data-id=\"1963fe31\" data-element_type=\"widget\" data-settings=\"{&quot;youtube_url&quot;:&quot;https:\\\/\\\/www.youtube.com\\\/watch?v=KNhkGZyUxwc&amp;t&quot;,&quot;video_type&quot;:&quot;youtube&quot;,&quot;controls&quot;:&quot;yes&quot;}\" data-widget_type=\"video.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-wrapper elementor-open-inline\">\n\t\t\t<div class=\"elementor-video\"><\/div>\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-ca3fe32 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"ca3fe32\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-5c8a21aa\" data-id=\"5c8a21aa\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-1d770fea elementor-align-center elementor-widget elementor-widget-button\" data-id=\"1d770fea\" data-element_type=\"widget\" data-widget_type=\"button.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<div class=\"elementor-button-wrapper\">\n\t\t\t\t\t<a class=\"elementor-button elementor-button-link elementor-size-md\" href=\"https:\/\/www.reseau-amylose.org\/jesuissoignant\/storage\/sites\/13\/2020\/10\/Amylose_Ordonnance-pour-rechercher-une-gammapathie-4.pdf\" target=\"_blank\">\n\t\t\t\t\t\t<span class=\"elementor-button-content-wrapper\">\n\t\t\t\t\t\t<span class=\"elementor-button-icon\">\n\t\t\t\t<i aria-hidden=\"true\" class=\"fas fa-edit\"><\/i>\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t<span class=\"elementor-button-text\">T\u00e9l\u00e9chargez l'ordonnance type pour rechercher une gammapathie<\/span>\n\t\t\t\t\t<\/span>\n\t\t\t\t\t<\/a>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-2b938a3 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"2b938a3\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-67ca646\" data-id=\"67ca646\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-9950c4a elementor-widget elementor-widget-heading\" data-id=\"9950c4a\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Pourquoi r\u00e9aliser des tests de gammapathie syst\u00e9matiquement en cas de suspicion d'amylose ?<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-f5703a2 elementor-widget elementor-widget-heading\" data-id=\"f5703a2\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h4 class=\"elementor-heading-title elementor-size-default\">Val\u00e9rie MOLINIER-FRENKEL<\/h4>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-3b659ab\" data-id=\"3b659ab\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-346d442 elementor-widget elementor-widget-video\" data-id=\"346d442\" data-element_type=\"widget\" data-settings=\"{&quot;youtube_url&quot;:&quot;https:\\\/\\\/www.youtube.com\\\/watch?v=wbUDfgZmhJU&amp;list=PLgcbJqP0xnzhFqwERU2_B1ltwSIBhKV0t&amp;index=27&quot;,&quot;video_type&quot;:&quot;youtube&quot;,&quot;controls&quot;:&quot;yes&quot;}\" data-widget_type=\"video.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-wrapper elementor-open-inline\">\n\t\t\t<div class=\"elementor-video\"><\/div>\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-f54d954 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"f54d954\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-66d953a\" data-id=\"66d953a\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-10fdb63 elementor-widget elementor-widget-heading\" data-id=\"10fdb63\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">A qui faire un test g\u00e9n\u00e9tique ?<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-0cea43e elementor-widget elementor-widget-text-editor\" data-id=\"0cea43e\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Le bilan biologique de l&rsquo;amylose aide au typage de l&rsquo;amylose. Un test g\u00e9n\u00e9tique doit \u00eatre fait pour tous les patients avec une amylose ATTR.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-4da5563 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"4da5563\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-eafb9f3\" data-id=\"eafb9f3\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-8b67de6 elementor-widget elementor-widget-video\" data-id=\"8b67de6\" data-element_type=\"widget\" data-settings=\"{&quot;youtube_url&quot;:&quot;https:\\\/\\\/www.youtube.com\\\/watch?v=lZa4zK3Zm-k&amp;list=PLgcbJqP0xnzhFqwERU2_B1ltwSIBhKV0t&amp;index=28&quot;,&quot;video_type&quot;:&quot;youtube&quot;,&quot;controls&quot;:&quot;yes&quot;}\" data-widget_type=\"video.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-wrapper elementor-open-inline\">\n\t\t\t<div class=\"elementor-video\"><\/div>\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-24f924f\" data-id=\"24f924f\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-21c8888 elementor-widget elementor-widget-heading\" data-id=\"21c8888\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Pour en savoir plus sur le bilan g\u00e9n\u00e9tique<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-fc45c8d elementor-align-center elementor-widget elementor-widget-button\" data-id=\"fc45c8d\" data-element_type=\"widget\" data-widget_type=\"button.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<div class=\"elementor-button-wrapper\">\n\t\t\t\t\t<a class=\"elementor-button elementor-button-link elementor-size-md\" href=\"https:\/\/reseau-amylose.org\/jesuissoignant\/aspects-genetiques-amylose\/\">\n\t\t\t\t\t\t<span class=\"elementor-button-content-wrapper\">\n\t\t\t\t\t\t\t\t\t<span class=\"elementor-button-text\">Cliquez ici<\/span>\n\t\t\t\t\t<\/span>\n\t\t\t\t\t<\/a>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-5b65f07 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"5b65f07\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-561169a\" data-id=\"561169a\" data-element_type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-7135371 elementor-widget elementor-widget-heading\" data-id=\"7135371\" data-element_type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">FAQ \u2014 Questions fr\u00e9quentes<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-6d13078 elementor-widget elementor-widget-toggle\" data-id=\"6d13078\" data-element_type=\"widget\" data-widget_type=\"toggle.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-toggle\">\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1141\" class=\"elementor-tab-title\" data-tab=\"1\" role=\"button\" aria-controls=\"elementor-tab-content-1141\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-left\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Pourquoi doser les biomarqueurs cardiaques dans l'amylose ?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1141\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"1\" role=\"region\" aria-labelledby=\"elementor-tab-title-1141\"><p>Parce que leur \u00e9l\u00e9vation t\u00e9moigne de la souffrance myocardique li\u00e9e \u00e0 l&rsquo;infiltration amylo\u00efde, et qu&rsquo;ils permettent d&rsquo;\u00e9tablir un score de gravit\u00e9 et de suivre la r\u00e9ponse au traitement, notamment dans l&rsquo;amylose AL.<\/p><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1142\" class=\"elementor-tab-title\" data-tab=\"2\" role=\"button\" aria-controls=\"elementor-tab-content-1142\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-left\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Quels examens r\u00e9aliser pour rechercher une gammapathie ?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1142\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"2\" role=\"region\" aria-labelledby=\"elementor-tab-title-1142\"><p>Une \u00e9lectrophor\u00e8se des protides, une immunofixation, un dosage des cha\u00eenes l\u00e9g\u00e8res libres s\u00e9riques et une recherche de prot\u00e9inurie de Bence Jones.<\/p><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1143\" class=\"elementor-tab-title\" data-tab=\"3\" role=\"button\" aria-controls=\"elementor-tab-content-1143\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-left\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">Faut-il faire un test g\u00e9n\u00e9tique chez tous les patients avec une amylose ATTR ?<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1143\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"3\" role=\"region\" aria-labelledby=\"elementor-tab-title-1143\"><p>Oui, un test g\u00e9n\u00e9tique du g\u00e8ne de la transthyr\u00e9tine doit \u00eatre r\u00e9alis\u00e9 syst\u00e9matiquement pour distinguer une forme h\u00e9r\u00e9ditaire d&rsquo;une forme sauvage.<\/p><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section class=\"elementor-section elementor-top-section elementor-element elementor-element-1a75cd7 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"1a75cd7\" data-element_type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-be5c928\" data-id=\"be5c928\" data-element_type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-f8e5b87 elementor-widget elementor-widget-text-editor\" data-id=\"f8e5b87\" data-element_type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Le bilan biologique de l&rsquo;amylose cardiaque repose sur trois volets compl\u00e9mentaires : le dosage des biomarqueurs cardiaques (peptides natriur\u00e9tiques, troponine), qui refl\u00e8tent la souffrance myocardique et guident le pronostic ; la recherche d&rsquo;une gammapathie monoclonale (\u00e9lectrophor\u00e8se des protides, immunofixation, cha\u00eenes l\u00e9g\u00e8res libres, prot\u00e9inurie de Bence Jones), indispensable pour diagnostiquer une amylose AL ; et le test g\u00e9n\u00e9tique du g\u00e8ne de la transthyr\u00e9tine, syst\u00e9matique chez tout patient porteur d&rsquo;une amylose ATTR pour distinguer forme h\u00e9r\u00e9ditaire et forme sauvage. Ce bilan participe directement au typage de l&rsquo;amylose, une \u00e9tape indispensable avant toute d\u00e9cision th\u00e9rapeutique.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<\/div>\n\t\t","protected":false},"excerpt":{"rendered":"<p>Le bilan biologique de l&rsquo;amylose Les examens compl\u00e9mentaires cardiaques permettent de suspecter l&rsquo;amylose. Seul le diagnostic anatomopathologique permet de l&rsquo;affirmer. L&rsquo;\u00e9chocardiographie, l&rsquo;IRM et la scintigraphie sont compl\u00e9mentaires dans l&rsquo;approche diagnostique, toutefois ces examens ne permettent pas de distinguer avec certitude les diff\u00e9rentes formes d&rsquo;amylose. Le bilan biologique de l&rsquo;amylose est important et participe au typage [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"parent":0,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"_acf_changed":false,"footnotes":""},"categories":[],"tags":[],"class_list":["post-3548","page","type-page","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v25.5 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Bilan biologique de l&#039;amylose cardiaque - R\u00e9seau Amylose<\/title>\n<meta name=\"description\" content=\"Biomarqueurs, recherche de gammapathie, test g\u00e9n\u00e9tique : le bilan biologique complet pour typer une amylose cardiaque.\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/reseau-amylose.org\/jesuissoignant\/examens-complementaires-electrocardiogramme-le-bilan-biologique-de-l-amylose\/\" \/>\n<meta property=\"og:locale\" content=\"fr_FR\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Bilan biologique de l&#039;amylose cardiaque - 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